histiocytic medullary reticulosis

A rapidly fatal lymphoma, characterized by fever, jaundice, pancytopenia, and enlargement of the liver, spleen, and lymph nodes. The affected organs show focal necrosis and hemorrhage, with proliferation of histiocytes and with phagocytosis of the red blood cells.

reticulosis [rĕ-tik″u-lo´sis]

an abnormal increase in cells derived from or related to the reticuloendothelial cells.

familial histiocytic reticulosis (histiocytic medullary reticulosis) a fatal hereditary disorder marked by anemia, granulocytopenia, thrombocytopenia, phagocytosis of blood cells, diffuse proliferation of histiocytes, and enlargement of the liver, spleen, and lymph nodes.

midline malignant reticulosis lethal midline granuloma thought to be due to lymphoma.

pagetoid reticulosis a solitary skin lesion of long duration and slow growth characterized histologically by large numbers of abnormal mononuclear cells infiltrating the epidermis with an underlying reactive mixed dermal infiltrate.

histiocytic lesion

An aggregate of histiocytes, which may be benign, indeterminant, or malignant in proliferative potential; to reduce confusion, it has been suggested that histiocytoses be subdivided into different categories

Histiocytic lesions-Behavior classification

Benign

• Familial histiocytosis with eosinophilia A chronic disease of infants with recurring bacterial infections, diarrhea, eczema, alopecia, associated with immunodeficiency

• Sinus histiocytosis with massive lymphadenopathy Rosai-Dorfman disease A disease most common in adolescent blacks with massive cervical lymphadenopathy as well as enlargement of extranodal (orbit, skin, bone, salivary gland, testis) lymphoid tissues

• Virus-associated hemophagocytic syndrome A condition induced by viral infections, often accompanied by abnormal liver function tests, coagulation assays and pancytopenia Pathology Histiocyte hyperplasia, hemophagocytosis and replacement of native bone marrow elements

Intermediate

• Histiocytosis X, aka Langerhans' cell histiocytosis, see there

• Reactive hemophagocytic syndrome, see there

Malignant

• Histiocytic medullary reticulosis see there

• Histiocytic proliferations, eg—acute monocytic leukemia (FAB M3), histiocytic lymphoma see there, malignant histiocytosis–see there

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Aarskog syndrome Adams-Stokes syndrome Adie's syndrome AEC syndrome afferent loop syndrome Ahumada-del Castillo syndrome Alagille syndrome Albright's syndrome Alport's syndrome amnestic syndrome ankyloblepharon-ectodermal dysplasia-clefting syndrome anterior cord syndrome Apert's syndrome de Lange's syndrome familial histiocytic reticulosis histiocytic lesion Kimmelstiel-Wilson syndrome Kugelberg-Welander syndrome reticulosis	histamine receptor antagonists histamine test histamine-fast histaminemia histaminergic histaminic headache histaminuria histenzyme histi(o)- histidase histidinase histidine histidine ammonia-lyase histidine decarboxylase histidinemia histidinuria histidyl histio- histioblast Histiocephalus histiocyte histiocytic histiocytic lesion histiocytic leukemia histiocytic malignant lymphoma histiocytic medullary reticulosis histiocytic necrotizing lymphadenitis histiocytoma histiocytosis histiocytosis X histiocytosis, acute disseminated, X histiocytosis, chronic disseminated X histiocytosis, Langerhans cell histiocytosis, nonlipid histiogenic histioid histiotypic growth histo- histoblast histochemistry histoclasia, implant histoclinical histocompatibility histocompatibility antigen Histocompatibility antigens histocompatibility complex histocompatibility gene histocompatibility locus histocompatibility testing histocompatibility typing histocyte	histiocyte histiocyte histiocyte Histiocyte Society Histiocyte-Rich B-Cell Lymphoma Histiocytes Histiocytes Histiocytes histiocytic histiocytic histiocytic histiocytic encephalitis histiocytic encephalitis histiocytic encephalitis histiocytic gastritis histiocytic gastritis histiocytic gastritis histiocytic lesion Histiocytic lesions-Behavior classification histiocytic leukaemia histiocytic leukemia histiocytic leukemia histiocytic leukemia histiocytic lymphocyte histiocytic lymphocyte histiocytic lymphocyte histiocytic lymphoma histiocytic lymphoma histiocytic lymphoma histiocytic malignant lymphoma histiocytic medullary reticulosis histiocytic necrotizing lymphadenitis Histiocytic proliferations, histiocytic ulcerative colitis histiocytic ulcerative colitis histiocytic ulcerative colitis histiocytoma histiocytoma Histiocytoma, malignant fibrous Histiocytoma, malignant fibrous histiocytoses histiocytoses histiocytoses histiocytosis histiocytosis histiocytosis Histiocytosis Association of America Histiocytosis with Joint Contractures and Sensorineural Deafness histiocytosis X histiocytosis X histiocytosis X histiocytosis, acute disseminated, X histiocytosis, chronic disseminated X histiocytosis, Langerhans cell Histiocytosis, malignant histiocytosis, nonlipid histiogenic histioid histioid Histiology Histioteuthidae

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