hexosaminidase B


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hex·os·a·min·i·dase B

[MIM*606873]
a hydrolytic enzyme that acts on ganglioside GM1, producing ganglioside GM1 and galactose, as well as on globoside, producing N-acetylgalactosamine and trihexosylceramide; a deficiency of this enzyme is associated with Sandhoff disease.