hepatolenticular degeneration - definition of hepatolenticular degeneration in the Medical dictionary - by the Free Online Medical Dictionary, Thesaurus and Encyclopedia.

degeneration /de·gen·er·a·tion/ (de-jen″er-a´shun) deterioration; change from a higher to a lower form, especially change of tissue to a lower or less functionally active form.degen´erative

ascending degeneration wallerian degeneration affecting centripetal nerve fibers and progressing toward the brain or spinal cord.

calcareous degeneration degeneration of tissue with deposit of calcareous material.

caseous degeneration caseation (2).

cerebromacular degeneration (CMD), cerebroretinal degeneration

1. degeneration of brain cells and of the macula retinae.

2. any lipidosis with cerebral lesions and degeneration of the macula retinae.

3. any form of neuronal ceroid-lipofuscinosis.

congenital macular degeneration hereditary macular degeneration with a cystlike lesion that in the early stages resembles egg yolk.

Crooke's hyaline degeneration Crooke's hyalinization.

descending degeneration wallerian degeneration extending peripherally along nerve fibers.

disciform macular degeneration a form of macular degeneration seen in persons over age 40, in which sclerosis involving the macula and retina is produced by hemorrhages between Bruch's membrane and the pigment epithelium.

fibrinous degeneration necrosis with deposit of fibrin within the cells of the tissue.

gray degeneration degeneration of the white substance of the spinal cord, in which it loses myelin and assumes a gray color.

hepatolenticular degeneration Wilson's disease.

hyaline degeneration a regressive change in cells in which the cytoplasm takes on a homogeneous, glassy appearance; also used loosely to describe the histologic appearance of tissues.

lattice degeneration of retina an often bilateral, usually benign asymptomatic condition, characterized by patches of fine gray or white intersecting lines in the peripheral retina, usually with numerous round punched-out areas of retinal thinning or retinal holes.

macular degeneration degenerative changes in the macula retinae.

mucoid degeneration that with deposit of myelin and lecithin in the cells.

myxomatous degeneration degeneration in which mucus accumulates in connective tissues.

spongy degeneration of central nervous system , spongy degeneration of white matter a rare hereditary form of leukodystrophy of early onset in which widespread demyelination and vacuolation of cerebral white matter gives it a spongy appearance; there is mental retardation, megalocephaly, atony of neck muscles, limb spasticity, and blindness, with death in infancy.

striatonigral degeneration a form of multiple system atrophy with nerve cell degeneration mainly in the region of the substantia nigra and the neostriatum; symptoms are similar to those of parkinsonism.

subacute combined degeneration of spinal cord degeneration of posterior and lateral columns of the spinal cord, with various motor and sensory disturbances; it is due to vitamin B12 deficiency and usually associated with pernicious anemia.

tapetoretinal degeneration degeneration of the pigmented layer of the retina.

transneuronal degeneration atrophy of certain neurons after interruption of afferent axons or death of other neurons to which they send their efferent output.

Zenker's degeneration hyaline degeneration and necrosis of striated muscle.

hep·a·to·len·tic·u·lar degeneration (h

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See Wilson's disease.

hepatolenticular degeneration

[həpat′ōlentik′yoo͡lər]

Etymology: Gk, hēpar + L, lens, lentil

an abnormal autosomal-recessive condition associated with defective copper metabolism in the body, characterized by decreased serum ceruloplasmin and copper levels and increased secretion of urinary copper. In individuals with this condition, tissue deposits of copper associated with hepatic cirrhosis, deep marginal pigmentation of the cornea (known as Kayser-Fleischer rings ), and extensive degeneration of the central nervous system, especially the basal ganglions, develop. Also called Wilson's disease.

hepatolenticular degeneration

Wilson's disease.

hepatolenticular degeneration

Wilson's disease, see there

Patient discussion about hepatolenticular degeneration.

Q. Hi this is Wilson; I have a daughter, who is 5. She has frequent nose bleeds when she is behaving badly. Hi this is Bell; I have a daughter, who is 5. She has frequent nose bleeds when she is behaving badly. She has been screened by her school for ADHD and I haven’t had a chance to consult a doctor for her screening and exam for ADHD. I thought that her nose bleeds cause due to her behavior? I need help.

A. I don’t have an idea about this. But I think that you should first discuss these issues with your doctor. Also mention to the doctor if she has any problems with sleeping, like only sleeping 6 hours a night. Try with occupational Therapists which help children and adults with small motor issues like handwriting and also with sensory issues like learning how to calm down. Early intervention is always best.