haemophilias

haemophilias

a group of inherited conditions in which blood coagulation is defective, resulting in an increased tendency to bleed, both spontaneously and as a result of trauma. For this reason, participation in contact sport is not advised.
References in periodicals archive ?
Haemophilias are distributed worldwide and have heterogeneous presentation depending upon its severity.
Haemophilia A (factor VIII deficiency) and haemophilia B (factor IX deficiency) are the most common and serious congenital coagulation factor deficiencies.
The bleeding episodes are treated with factor replacement therapy with either factor VIII for haemophilia A and factor IX for haemophilia B or with cryoprecipitate or fresh frozen plasma.
Historically, the haemophilias were all considered to be one entity until detailed blood separation techniques allowed more in-depth analyses and categorisation.
Haemophilia is a serious medical condition, resulting in prolonged or intensive episodes of bleeding.
haemophilia, with an emphasis on the ocular presentations that may be seen in both diagnosed and
Inhibitor treatment in haemophilias A and B: summary statement for the 2006 international consensus conference.
Background: Haemophilia B is X-linked recessive inherited disorder of factor IX deficiency.
Patients and Methods: Total 45 patients of Haemophilia B already enrolled in the Haemophilia society of Pakistan Lahore chapter were included in this study.
Haemophilia A and B are rare inherited bleeding disorders characterized in the most severe form by spontaneous bleeding into joint and muscles associated with invalidating arthropathy, as well as by more serious bleeds, namely intracranial haemorrhage (1).
The haemophilia comprehensive care model, which is defined as the continuing supervision of all medical and psychosocial factors affecting patients and their families, has been a cornerstone and one of the most successful health programmes in developed countries, resulting in a significant improvement of health and, ultimately, of life expectancy for haemophilia community (6,7).
The World Federation of Haemophilia (WFH) is a non-profit organization founded in 1963 with the aim of improving global haemophilia care to all people with haemophilia, wherever they live.