malignant solitary fibrous tumour

(redirected from haemangiopericytoma)

malignant solitary fibrous tumour

An uncommon soft tissue malignancy (66% to 90% of SFTs are benign), most of which arise in the pleura. Extrapleural SFTs are even rarer, with about 100 having been reported in the world literature, arising in the meninges, orbit, upper respiratory tract, salivary glands, thyroid, peritoneum, liver, retroperitoneum, adrenal gland, kidney, spermatic cord, urinary bladder and prostate spinal cord, periosteum and soft tissue, mainly in the head and neck.
 
DiffDx
Haemangiopericytoma, synovial sarcoma, dermatofibrosarcoma protuberans, leiomyosarcoma, liposarcoma, malignant peripheral nerve sheath tumour.

Management
Excision, radiation therapy.
References in periodicals archive ?
1,2) Of these, leiomyosarcoma is the most common type (50%-60%), followed by liposarcoma, haemangiopericytoma, fibrosarcomas, malignant fibrous histiocytomas, and rhabdomyosarcoma.
Pathological and radiological differential diagnosis Small round blue cell tumour Radiological Non-Hodgkin's lymphoma Rhabdomyosarcoma Rhabdomyosarcoma Myosarcoma Small cell lung cancer Malignant fibrous Merkel cell cancer histiocytoma (MFH) Haemangiopericytoma Dedifferentiated liposarcoma Neuroblastoma Ewing's sarcoma Ewing's sarcoma Primitive neuro-ectodermal tumour (PNET)
Differential diagnoses must include multiple variants of meningiomas, renal cell carcinoma, and haemangiopericytoma (4,5,8,9).
Hypoglycaemia associated with the production of insulin-like growth factor II and insulin-like growth factor binding protein 6 by a haemangiopericytoma.
Haemangiopericytoma of the nasal cavity in Ibadan, Nigeria.