malignant solitary fibrous tumour

(redirected from haemangiopericytoma)

malignant solitary fibrous tumour

An uncommon soft tissue malignancy (66% to 90% of SFTs are benign), most of which arise in the pleura. Extrapleural SFTs are even rarer, with about 100 having been reported in the world literature, arising in the meninges, orbit, upper respiratory tract, salivary glands, thyroid, peritoneum, liver, retroperitoneum, adrenal gland, kidney, spermatic cord, urinary bladder and prostate spinal cord, periosteum and soft tissue, mainly in the head and neck.
 
DiffDx
Haemangiopericytoma, synovial sarcoma, dermatofibrosarcoma protuberans, leiomyosarcoma, liposarcoma, malignant peripheral nerve sheath tumour.

Management
Excision, radiation therapy.
References in periodicals archive ?
5 to 70 years (Mean Age=11y), 6 (3M, 3F) were soft tissue sarcomas with ages between 15 and 75 years (Mean Age=43y), 4 (3M, 1F) osteosarcomas, ages 20 to 45 years (Mean Age=27y) and 3 vascular in origin; 2 (M) Malignant Haemangiopericytoma, ages 35 and 40 years and 1 (M) Malignant Angioma with age 40 years.
Haemangiopericytoma of left 5th rib with intraspinal extension causing D5 vertebral collapse and secondary aneurysmal bone cyst.
Haemangiopericytoma of the maxillary gingiva: report of a case.
1,2) Of these, leiomyosarcoma is the most common type (50%-60%), followed by liposarcoma, haemangiopericytoma, fibrosarcomas, malignant fibrous histiocytomas, and rhabdomyosarcoma.
Haemangiopericytoma is a very rare tumour of the Zimmermann pericyte.
Pathological and radiological differential diagnosis Small round blue cell tumour Radiological Non-Hodgkin's lymphoma Rhabdomyosarcoma Rhabdomyosarcoma Myosarcoma Small cell lung cancer Malignant fibrous Merkel cell cancer histiocytoma (MFH) Haemangiopericytoma Dedifferentiated liposarcoma Neuroblastoma Ewing's sarcoma Ewing's sarcoma Primitive neuro-ectodermal tumour (PNET)
Haemangiopericytoma are a variety of soft tissue sarcomas which are vascular in origin and consist of pericytes5.
Differential diagnoses must include multiple variants of meningiomas, renal cell carcinoma, and haemangiopericytoma (4,5,8,9).
The histopathological evaluation confirmed haemangiopericytoma by immunohistochemistry.
Hypoglycaemia associated with the production of insulin-like growth factor II and insulin-like growth factor binding protein 6 by a haemangiopericytoma.
The differential diagnosis after ultrasound examination included liposarcoma, haemangiopericytoma and leiomyosarcoma.
Differential diagnosis includes meningioma of the neck, metastatic meningioma to thyroid, haemangiopericytoma, medullary carcinoma, solitary fibrous tumour and other vascular and spindle cell lesions of the thyroid.