hemangioblastoma

(redirected from haemangioblastoma)
Also found in: Dictionary.

hemangioblastoma

 [he-man″je-o-blas-to´mah]
a benign blood vessel tumor of the cerebellum, spinal cord, or retina, consisting of proliferated blood vessel cells and angioblasts. Those arising in the cerebellum (cerebellar hemangioblastoma) may be cystic and associated with von hippel-lindau disease. Called also angioblastoma.
cerebellar hemangioblastoma hemangioblastoma of the cerebellum, often cystic; an autosomal dominant form is associated with von Hippel-Lindau disease.

he·man·gi·o·blas·to·ma

(he-man'jē-ō-blas-tō'mă),
A benign neoplasm frequently arising in the cerebellum composed of capillary vessel-forming endothelial cells and stromal cells; a slowly growing tumor that affects, primarily, middle-aged individuals; increased incidence in von Hippel-Lindau disease.

hemangioblastoma

/he·man·gio·blas·to·ma/ (he-man″je-o-blas-to´mah) a benign blood vessel tumor of the cerebellum, spinal cord, or retina, consisting of proliferated blood vessel cells and angioblasts.

hemangioblastoma

[hēman′jē·ōblastō′mə] pl. hemangioblastomas, hemangioblastomata
Etymology: Gk, haima + angeion, vessel, blastos, germ, oma, tumor
a brain tumor composed of a proliferation of capillaries and of disorganized clusters of capillary cells or angioblasts, usually occurring in the cerebellum.

Hemangioblastoma

(1) A tumour of soft tissues, which is of intermediate aggressiveness and thus preferably known as hemangioendothelioma.
(2) A vascularised cerebellar tumour, representing 2% of CNS neoplasms, which occurs in the 3rd–4th decades, either alone or associated with von-Hippel-Lindau syndrome, phaeochromocytoma, syringomyelia or erythrocythemia. 

Management
Excision.
 
Prognosis
Good.

he·man·gi·o·blas·to·ma

(hē-man'jē-ō-blas-tō'mă)
A benign cerebellar neoplasm composed of capillary vessel-forming endothelial cells and stromal cells; a slowly growing tumor that affects, primarily, middle-aged individuals; increased incidence in von Hippel-Lindau disease.
Synonym(s): angioblastoma, Lindau tumor, haemangioblastoma.

Lindau,

Arvid Wilhelm, Swedish pathologist, 1892-1958.
Lindau disease - Synonym(s): von Hippel-Lindau syndrome
Lindau tumor - a benign cerebellar neoplasm. Synonym(s): hemangioblastoma
von Hippel-Lindau syndrome - see under von Hippel
References in periodicals archive ?
Pathology was a dural-based WHO Grade 1 supratentorial haemangioblastoma.
These were later revised in the 1990's by neuropathologists Russel and Rubinstein, classifying the variant 3 into haemangioblastoma (3 ).
In conclusion, this is a unique case of a supratentorial haemangioblastoma that should be on the differential diagnosis of dural-based tumors in patients of Native American descent who are without Von Hippel Lindau syndrome.
The association with Von Hippel Lindau Syndrome demonstrates multiple haemangioblastomas, usually infratentorially, and has an autosomal dominant genetic transmission on chromosome 3 (8).
Metastasis of renal cell carcinoma to haemangioblastoma of the spinal cord in von Hippel-Lindau disease: case report and review of the literature.
Histological differentiation of metastatic renal carcinoma in the cerebellum from cerebellar haemangioblastoma in von Hippel-Lindau's disease.
A case of cystic form of angiomatous meningioma with prominent microvascular pattern mimicking haemangioblastoma.