giant-cell fibroblastoma

giant-cell fibroblastoma

A rare solitary mesenchymal tumour, classified by the WHO as a fibrohistiocytic tumour of intermediate malignancy, which is related to dermatofibrosarcoma protuberans.

Clinical findings
Occurs in children, usually under age 5, often in the superficial soft tissues of the thigh, back, sacrum and inguinal region.

Management
Best option for cure is careful resection of margins with Moh’s surgery.

Prognosis
Locally aggressive, up to 50% recurrence; does not metastasise.
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