low-grade fibromyxoid sarcoma

(redirected from fibromyxoid type fibrosarcoma)

low-grade fibromyxoid sarcoma

low-grade malignant tumor of soft tissues of proximal extremities or trunk, composed of fibroblasts forming myxoid areas or surrounding giant collagen rosettes.

low-grade fibromyxoid sarcoma

A rare, deep soft-tissue sarcoma of young adults with a deceptively bland appearance, which is characterised by local recurrences and, eventually, metastases to lung and bone.

DiffDx Benign
Deep fibromatosis, nodular fasciitis.

DiffDx Malignant
Leiomyosarcoma, myofibrosarcoma, sclerosing epithelioid fibrosarcoma, low-grade fibrosarcoma, classic fibrosarcoma, inflammatory myxohyaline/myxoinflammatory fibroblastic sarcoma.

Prognosis
Local recurrence, 9%; metastases, 6%; death, 2%.