familial histiocytic reticulosis

reticulosis /re·tic·u·lo·sis/ (rĕ-tik″u-lo´sis) an abnormal increase in cells derived from or related to the reticuloendothelial cells.

familial histiocytic reticulosis , histiocytic medullary reticulosis a fatal hereditary disorder marked by anemia, granulocytopenia, thrombocytopenia, phagocytosis of blood cells, diffuse proliferation of histiocytes, and enlargement of the liver, spleen, and lymph nodes.

malignant midline reticulosis , polymorphic reticulosis a form of angiocentric immunoproliferative lesion involving midline structures of the nose and face.

Etymology: L, familia, household; Gk, histion, web, kytos, cell; L, reticulum, little net; Gk, osis, condition

a hereditary disease, transmitted as an autosomal-recessive trait, characterized by anemia, granulocytopenia, and thrombocytopenia. Phagocytosis of blood cells and infiltration of bone marrow by histiocytes commonly cause death in childhood. Also called familial hemophagocytic reticulosis.

reticulosis [rĕ-tik″u-lo´sis]

an abnormal increase in cells derived from or related to the reticuloendothelial cells.

familial histiocytic reticulosis (histiocytic medullary reticulosis) a fatal hereditary disorder marked by anemia, granulocytopenia, thrombocytopenia, phagocytosis of blood cells, diffuse proliferation of histiocytes, and enlargement of the liver, spleen, and lymph nodes.

midline malignant reticulosis lethal midline granuloma thought to be due to lymphoma.

pagetoid reticulosis a solitary skin lesion of long duration and slow growth characterized histologically by large numbers of abnormal mononuclear cells infiltrating the epidermis with an underlying reactive mixed dermal infiltrate.

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histiocytic medullary reticulosis reticulosis	falx inguinalis falx ligamentosa FAM famciclovir famcyclovir familial familial adenomatous polyposis familial aggregation familial Alzheimer's disease familial amyloidosis familial autonomic dysfunction familial benign chronic pemphigus familial broad-beta hyperlipoproteinemia familial centrolobar sclerosis familial combined hyperlipidemia familial cretinism familial dysautonomia familial dysbetalipoproteinemia familial exudative vitreoretinopathy familial fat-induced hyperlipemia Familial Fatal Insomnia familial focal facial dermal dysplasia familial hemiplegic migraine familial Hibernian fever familial high-density lipoprotein deficiency familial histiocytic reticulosis familial hyperbetalipoproteinemia familial hyperbetalipoproteinemia and hyperprebetalipoproteinemia familial hypercholesterolemia familial hypercholesterolemia with hyperlipemia familial hyperchylomicronemia familial hyperchylomicronemia with hyperprebetalipoproteinemia familial hyperglyceridemia familial hyperlipoproteinemia familial hyperprebetalipoproteinemia familial hypertriglyceridemia familial hypertrophic cardiomyopathy familial iminoglycinuria familial intestinal polyposis familial intraosseous fibrous swelling of the jaws familial juvenile nephronophthisis familial juvenile nephrophthisis familial lipoprotein lipase deficiency familial malignancy familial Mediterranean fever familial multiple endocrine familial nonhemolytic jaundice familial osteochondrodystrophy familial paroxysmal polyserositis familial periodic fever familial periodic paralysis	familial factor familial factor familial fat-induced hyperlipemia familial fat-induced hyperlipemia familial fat-induced hyperlipemia Familial fatal insomnia Familial fibrous dysplasia of jaw Familial Fibrous Dysplasia of the Jaw Familial Fibrous Dysplasia of the Jaws Familial Fibrous Jaw Dysplasia Familial Fibrous Swelling of Jaw familial focal facial dermal dysplasia familial glomerulonephritis familial glomerulonephritis familial glomerulonephritis Familial Glucocorticoid Deficiency Familial HDL Deficiency familial hemiplegic migraine familial hemiplegic migraine Familial hemochromatosis Familial Hemophagocytic Lymphohistiocytosis Familial Hemophagocytic Lymphohistocytosis Familial Hibernian fever Familial High Density Lipoprotein Deficiency Disease familial high-density lipoprotein (HDL) deficiency familial high-density lipoprotein (HDL) deficiency familial high-density lipoprotein (HDL) deficiency familial high-density lipoprotein (HDL) deficiency familial high-density lipoprotein (HDL) deficiency familial high-density lipoprotein deficiency familial histiocytic reticulosis familial histiocytic reticulosis, histiocytic medullary reticulosis familial histiocytic reticulosis, histiocytic medullary reticulosis Familial histiocytosis with eosinophilia Familial History of Breast Carcinoma Familial Horizontal Gaze Palsy with Progressive Scoliosis Familial Hyperaldosteronism Type I familial hyperbetalipoproteinemia familial hyperbetalipoproteinemia and hyperprebetalipoproteinemia Familial hypercalcemia with nephrocalcinosis and indicanuria Familial Hypercholanemia Familial hypercholesterolaemia Familial hypercholesterolaemia familial hypercholesterolemia familial hypercholesterolemia familial hypercholesterolemia with hyperlipemia familial hyperchylomicronemia familial hyperchylomicronemia with hyperprebetalipoproteinemia familial hyperglyceridemia Familial Hyperkalemic Periodic Paralysis familial hyperlipoproteinemia familial hyperprebetalipoproteinemia Familial Hyperreninemic Hypoaldosteronism familial hypertriglyceridemia familial hypertriglyceridemia familial hypertrophic cardiomyopathy familial hypertrophic cardiomyopathy Familial Hypoalphalipoproteinemia Familial hypobetalipoproteinemia Familial hypobetalipoproteinemia Familial hypobetalipoproteinemia

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histiocytic medullary reticulosis
reticulosis

familial adenomatous polyposis

familial aggregation