erythrokeratodermia

erythrokeratodermia

 [ĕ-rith″ro-ker″ah-to-der´-me-ah]
reddening and hyperkeratosis of the skin.
erythrokeratodermia varia´bilis a rare, dominantly inherited ichthyosis characterized by circumscribed areas of erythema that undergo changes in size, shape, and distribution over a period of days, with plaques of yellow-brown scales that occur in the areas of erythema. The usual onset is at birth or in the first year of life, and the disease runs a chronic course with remissions and exacerbations.

e·ryth·ro·ker·a·to·der·mi·a

(ĕ-rith'rō-ker-ă-tō-der'mē-ă), [MIM*133190]
A neurocutaneous syndrome characterized by papulosquamous erythematous plaques with onset shortly after birth; ataxia, nystagmus, dysarthria, and decreased tendon reflexes appear later in life; symmetric progressive erythrokeratodermia is inherited as an autosomal dominant disorder and does not involve the palms and soles.
[erythro- + G. keras, horn, + derma, skin, + -ia, condition]

erythrokeratodermia

/eryth·ro·ker·a·to·der·mia/ (ĕ-rith″ro-ker″ah-to-der´me-ah) a reddening and hyperkeratosis of the skin.
erythrokeratodermia varia´bilis  a rare hereditary form of ichthyosis marked by transient, migratory areas of discrete, macular erythroderma as well as fixed hyperkeratotic plaques.

e·ryth·ro·ker·a·to·der·mi·a

(ĕ-rith'rō-ker-ă-tō-dĕr'mē-ă)
A neurocutaneous syndrome characterized by papulosquamous erythematous plaques with onset shortly after birth; ataxia, nystagmus, dysarthria, and decreased tendon reflexes appear later in life; symmetric progressive erythrokeratodermia is inherited as an autosomal dominant disorder and does not involve the palms and soles.
[erythro- + G. keras, horn, + derma, skin, + -ia, condition]

erythrokeratodermia

a reddening and hyperkeratosis of the skin.
References in periodicals archive ?
PUVA helps over 50 conditions, ranging from mycosis fungoides to erythrokeratodermia progressiva symmetrica.
com 1,2,3,4,5,6 ERB/DUCHENNE PALSY See: Erb Palsy ERDHEIM-CHESTER DISEASE See: Histiocytosis ERYTHROBLASTOPHTHISIS See: Anemia, Aplastic ERYTHROBLASTOTIC ANEMIA OF CHILDHOOD See: Cooley Anemia ERYTHROID HYPOPLASIA, CONSTITUTIONAL See: Anemia, Diamond-Blackfan ERYTHROHEPATIC PROTOPORPHYRIA See: Liver Disorders; Porphyria ERYTHROKERATODERMIAS See: Ichthyosis ERYTHROPHAGOCYTIC LYMPHOHISTIOCYTOSIS, FAMILIAL See: Histiocytosis ESOPHAGEAL ATRESIA See: VATERL Association EVANS SYNDROME See also: Autoimmune Disorders; Neutropenia Evans Syndrome Support and Research Group c/o Lou Addington 5630 Devon St.
com 1,2,3,4,5,6 ERB/DUCHENNE PALSY See: Erb Palsy ERDHEIM-CHESTER DISEASE See: Histiocytosis ERYTHROBLASTOPHTHISIS See: Anemia, Aplastic ERYTHROBLASTOTIC ANEMIA OF CHILDHOOD See: Cooley Anemia ERYTHROHEPATIC PROTOPORPHYRIA See: Liver Disorders; Porphyria ERYTHROKERATODERMIAS See: Ichthyosis ERYTHROPHAGOCYTIC LYMPHOHISTIOCYTOSIS, FAMILIAL See: Histiocytosis ESOPHAGEAL ATRESIA See: VATERL Association EVANS SYNDROME See also: Autoimmune Disorders; Neutropenia Evans Syndrome Support and Research Group c/o Lou Addington 5630 Devon St.