epidermodysplasia


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epidermodysplasia

 [ep″ĭ-der″mo-dis-pla´zhah]
faulty development of the epidermis.
epidermodysplasia verrucifor´mis the widespread and persistent (sometimes lasting decades) dissemination of verruca plana associated with a tendency to malignant degeneration. It typically begins in early childhood with the development of flat-topped papules that increase in number and coalesce to form large plaques, especially on the knees, elbows, and trunk. Familial occurrence and mental retardation are often associated with the disorder.

ep·i·der·mo·dys·pla·si·a

(ep'i-dĕr'mō-dis-plā'zē-ă),
Faulty growth or development of the epidermis.
[epidermis + G. dys-, bad, + plasis, a molding]

epidermodysplasia

/epi·der·mo·dys·pla·sia/ (-der″mo-dis-pla´zhah) faulty development of the epidermis.
epidermodysplasia verrucifor´mis  a condition due to a virus identical with or closely related to the virus of common warts, in which the lesions are red or red-violet and widespread, and tend to become malignant.

ep·i·der·mo·dys·pla·si·a

(ep'i-dĕr'mō-dis-plā'zē-ă)
Faulty growth or development of the epidermis.
[epidermis + G. dys-, bad, + plasis, a molding]

epidermodysplasia

see epidermal dysplasia.
References in periodicals archive ?
Discovered in the Indonesian jungle, the skin disorder epidermodysplasia verruciformis (EV) has been found only in individuals of Indonesian and Dutch-Indonesian descent.
Recurrent 'sterile' verrucous cyst abscesses and epidermodysplasia verruciformis-like eruption with idiopathic CD4 lymphopenia.
Eight papers examine these developments from such perspectives as clinical manifestations of hyper IgE syndromes, the essential role of DOCK8 in humoral immunity, DOCK8 immune deficiency as a model for primary cytoskeletal dysfunction, and epidermodysplasia verruciformis and the susceptibility to HPV.
Patients with epidermodysplasia verruciformis have an immune defect that prevents recognition of HPV, resulting in severe skin infection and a 90% increase in NMSC risk (Pfister 2003).
High frequency of detection of human papillomaviruses associated with epidermodysplasia verruciformis in children with psoriasis.
Treatment of localized epidermodysplasia verruciformis with tacalcitol ointment.
The link between [beta]-HPV and skin cancer was first identified in patients with epidermodysplasia verruciformis (EV), a rare genetic condition characterized by skin lesions on sun-exposed areas and an abnormal sensitivity to specific HPV types.
Age, y Sex Diagnosis 1 57 M MCC, primary 2 61 F MCC, primary 3 57 F MCC, primary 4 82 F MCC, primary 5 78 M MCC, metastatic 6 80 F MCC, primary 7 65 M MCC, primary 8 81 M MCC, primary 9 60 M MCC, primary 10 61 M Hyperkeratosis 11 49 M Seborrheic keratosis, penis 12 60 M Nonspecific lesion, esophagus 13 40 M Nasal papilloma 14 58 M Anal condylomas 15 44 M Epidermodysplasia verruciformis 16 19 M Cutaneous warts 17 57 F Cutaneous warts 18 64 F Cutaneous nodule 19 6 F Pharyngeal papillomatosis 20 27 M Vocal cord polyp 21 58 M Lichen 22 63 M Skin inflammation 23 72 M Skin inflammation 24 57 M Skin inflammation Patient no.
Favre M, Orth G, Majewski S, Baloul S, Pura A, Jablonska S: Psoriasis: A possible reservoir for human papillomavirus type 5, the virus associated with skin carcinomas of epidermodysplasia verruciformis.
Other clinical presentations of HPV include bowenoid papulosis and epidermodysplasia verruciformis.
Research so far has identified increased risks for people with skin HPV types called beta HPVs, particularly among organ transplant recipients and people with epidermodysplasia verruciformis (EV) - a rare genetic disorder, which leads to warts and malignant skin lesions.
6, 11, 16, 30, 33, 36, 37, 38, epidermoid cysts, laryngeal 41, 48, 60, 72, 73 carcinoma) Epidermodysplasia verruciformis 2, 3, 10, 5, 8, 9, 12, 14, 15, 17, 19, 20, 21, 22, 23, 24, 25, 36, 37, 37, 47, 50 Recurrent respiratory 6, 11 papillomatosis Focal epithelial hyperplasia of 13, 32 heck Conjunctival papillomas/ 6, 11, 16 carcinomas Condyloma acuminata (genital 6, 11, 30, 42, 43, 45, 51, 54, warts) 55, 70 Data from Ref.