embryonal rhabdomyosarcoma


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em·bry·o·nal rhab·do·my·o·sar·co·ma

malignant neoplasm occurring in children, consisting of loose, spindle-celled tissue with rare cross-striations, and arising in many parts of the body in addition to skeletal muscles.
References in periodicals archive ?
2) Embryonal rhabdomyosarcomas have a poor prognosis irrespective of therapy, (4,5) as seen in the present case.
5: Immunohistochemical staining of embryonal rhabdomyosarcoma with myogenin.
Sukov and coworkers (11) found ALK gene rearrangements in 67% of tumors in a series that included 21 cases of IMTs of the urinary bladder, but found no such ALK gene rearrangement in the other tumors among 32 non-IMTs tested, including 16 leiomyosarcomas and 3 embryonal rhabdomyosarcomas.
In this article, the author reports a case of embryonal rhabdomyosarcoma of the temporal bone with cranial nerve palsies and extension into the parapharyngeal space.
In 1998, at age 11 months, he was diagnosed with embryonal rhabdomyosarcoma of the right maxilla and underwent partial maxillectomy and temporal bone resection, followed by chemotherapy (vinblastine) and radiation therapy.
The histopathologic features of the biopsy specimen were consistent with an embryonal rhabdomyosarcoma (figure 1).
We recommend that embryonal rhabdomyosarcoma be ruled out to avoid overly aggressive treatment of these patients.
Embryonal rhabdomyosarcoma is the most common histologic variant seen in childhood; a large proportion of them arise in the head and neck-most commonly in the orbit, the nasopharynx, and the ear.