dermatofibrosis lenticularis disseminata

der·ma·to·fi·bro·sis len·tic·u·lar·is dis·sem·i·na·ta

(der'mă-tō-fī-brō'sis len-tik'yū-lā'ris di-sem'i-nā'tă), [MIM*166700]
Small papules or disks of increased dermal elastic tissue appearing in early life; when osteopoikilosis is also present, the condition is called osteodermatopoikilosis or Buschke-Ollendorf syndrome; autosomal dominant inheritance.
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Various developmental malformations have been reported to be associated with osteopoikilosis, including: coarctation of the aorta, double ureter, pubertas praecox, urogenital defects, growth abnormalities, peptic ulcer, diabetes mellitus at the endodermal strata level; arthritis, exostoses, osteitis condensans ilii, Klippel-Feil Syndrome, melorheostosis, spinal stenosis, cervical myelopathy, dacryocystitis, giant cell tumor, fibrous dysplasia, chondrosarcoma, osteosarcoma, synovial chondromatosis at the mesodermal level; facial abnormalities, hare lip, dental abnormalities, dermatofibrosis lenticularis disseminata, keloid formation, plantar and palmar keratomas at the ectodermal level (14-16).
1,2) Several clinical abnormalities associated with OPK have been reported, including rheumatoid arthritis, synovial chondromatosis, and, more frequently, dermatological pathologies (such as dermatofibrosis lenticularis disseminata, keloid formations and scleroderma-like lesions).
Dermatofibrosis lenticularis disseminata and osteopoikilosis [in German].