Congenital cystic adenomatoid malformation
type 3 is a rare tumorlike lung malformation.
Congenital cystic adenomatoid malformation of the lung (CCAM) is an uncommon condition characterized by cysts of various sizes lined by bronchiolar- or alveolar-like epithelium.
Congenital cystic adenomatoid malformation of the lung (CCAM): evaluation of the cellular components.
Elevated platelet-derived growth factor-B in congenital cystic adenomatoid malformations requiring fetal resection.
Stocker JT, Madewell JE, Drake RM: Congenital cystic adenomatoid malformation
of the lung.
112,113) Mucinous cells in pulmonary congenital cystic adenomatoid malformation
share the same differentiation profile (including the expression of MUC5AC) and molecular abnormalities (frequent K-ras mutation) as mBAC and can then be considered as a precursor lesion of this entity.
Of four cases with cardiac malposition caused by extracardiac congenital malformation,two cases had mesoposition dueto pleural effusion, one case had dextroposition due to left-sided congenital diaphragmatic hernia, and one case had an extreme levoposition due to cystic adenomatoid malformation
in the right lung (Table 1).
Outcome and treatment in an antenatally diagnosed congenital cystic adenomatoid malformation of the lung.
Congenital cystic diseases of the lung and mediastinum include congenital cystic adenomatoid malformation (CCAM), bronchopulmonary "sequestration", congenital lobar emphysema, broncogenic cyst, esophageal duplication cysts and neurogenic cysts (1).
Development of hydrops due to congenital cystic adenomatoid malformation can be predicted in the prenatal period by calculating CCAM volume ratio (CVR) on USG.
Antenatal diagnosis and management of congenital cystic adenomatoid malformation.
Congenital cystic adenomatoid malformation is an embrionic developmental disorder characterized by cystic enlargement and overgrowth of terminal bronchioles which are surrounded by various epithelial cells.