Coproporphyrinogen oxidase | definition of coproporphyrinogen oxidase by Medical dictionary
Also found in: Acronyms
an enzyme that catalyzes a step in porphyrin biosynthesis, reacting coproporphyrinogen III and O2 to form protoporphyrinogen IX and 2CO2. A deficiency of this enzyme will result in hereditary coproporphyria.
References in periodicals archive
The excessive urinary coproporphyrin excretion cannot be caused by an enzymatic deficiency, because coproporphyrinogen oxidase
activity was within reference values.