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congenital ichthyosiform erythroderma

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erythroderma /eryth·ro·der·ma/ (-der´mah) abnormal redness of the skin over widespread areas of the body.erythroder´mic
congenital ichthyosiform erythroderma  a generalized hereditary dermatitis with scaling, which occurs in bullous (epidermolytic hyperkeratosis) and nonbullous (lamellar ichthyosis) forms.
erythroderma desquamati´vum  Leiner's disease.
erythroderma psoria´ticum  erythrodermic psoriasis.

congenital ichthyosiform erythroderma or ichthyosiform erythroderma
n.
A hereditary skin disease characterized by diffuse chronic erythema and the formation of thickened, scaly skin on the palms and soles, sometimes associated with ocular and neural changes.

erythroderma [ĕ-rith″ro-der´mah]
abnormal redness of the skin over widespread areas of the body.
congenital ichthyosiform erythroderma a generalized hereditary dermatitis with scaling, occurring in a bullous form (epidermolytic hyperkeratosis) and a nonbullous form (lamellar ichthyosis).
erythroderma desquamati´vum Leiner's disease.
psoriatic erythroderma a generalized psoriasis vulgaris, showing the chemical characteristics of exfoliative dermatitis.


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Congenital ichthyosiform erythroderma is one of the severe ichthyoses for which no therapy is commercially available.
 
 
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