ALG1

(redirected from chitobiosyldiphosphodolichol beta-mannosyltransferase)

ALG1

A gene on chromosome 16p13.3 that encodes an enzyme that catalyses the first mannosylation step in the biosynthesis of lipid-linked oligosaccharides.

Molecular pathology
ALG1 is mutated in congenital disorder of glycosylation type Ik (CDGIk).