ceramide (redirected from ceramide lactosidosis)

ceramide /cer·a·mide/ (ser´ah-mid) the basic unit of the sphingolipids; it is sphingosine, or a related base, attached to a long chain fatty acyl group. Ceramides are accumulated abnormally in Farber's disease.

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ceramide trihexoside  any of a specific family of glycosphingolipids; due to a deficiency of a-galactosidase A, they accumulate in Fabry's disease.

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cer·am·ide (s-rmd, sûr-md)

n.

Any of a group of amides formed by linking a fatty acid to sphingosine and found in plant and animal tissue.

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ceramide

any of a group of naturally occurring sphingolipids in which the NH₂ group of sphingosine is acylated with a fatty acyl CoA derivative to form N-acylsphingosine.

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ceramide glucoside

the major sphingolipid accumulated in gaucher's disease.

ceramide lactosidosis

a sphingolipidosis in which ceramide lactoside accumulates in neural and visceral tissues owing to a deficiency of a ß-galactosidase.