carbamoyltransferase

carbamoyltransferase

 [kahr″bah-moil-trans´fer-ās]
an enzyme that catalyzes the transfer of carbamoyl, as from carbamoylphosphate to l-ornithine to form orthophosphate and citrulline in the synthesis of urea.

carbamoyltransferase

/car·bam·o·yl·trans·fer·ase/ (kahr-bam″o-il-trans´fer-ās) an enzyme that catalyzes the transfer of a carbamoyl group, as from carbamoylphosphate to l-ornithine to form orthophosphate and citrulline in the synthesis of urea.

carbamoyltransferase

see ornithine carbamoyl transferase.
References in periodicals archive ?
Nearly all of the proteins altered in significant amounts were identified as enzymes associated with important metabolic pathways, such as alcohol dehydrogenase, glyceraldehyde-3-phosphate dehydrogenase (GAPDH), Xaa-His dipeptidase, ornithine carbamoyltransferase, putative O-acetylserine lyase, enolase (2-phosphoglycerate dehydratase), fructose-bisphosphate aldolase, and cysteine synthase.
7] Human genes: CPS1, carbamoyl-phosphate synthetase 1, mitochondrial; NAGS, N-acetylglutamate synthase; OTC, ornithine carbamoyltransferase.
Tamir and Ratner (1963) attributed birds' incapacity to synthesize ornithine, citrulline and Arg to the absence of another enzyme key to the urea cycle, ornithine carbamoyltransferase (Figure 2).
2 carbamoyltransferase Phosphoenolpyruvate NM_174737.
This dramatic case stumped physicians until the woman's blood revealed a telltale high level of ammonia, a diagnostic clue suggesting a rare, inherited disorder called ornithine carbamoyltransferase deficiency.
All carried the mutant gene causing ornithine carbamoyltransferase deficiency, and two of the five subsequently died.
Mutation detection in 65 families with a possible diagnosis of ornithine carbamoyltransferase deficiency including 14 novel mutations.
The genes surrounding the GK gene, from telomere to centromere, are Xpter-interleukin 1 receptor accessory protein-like 1 (IL1RAPL1); nuclear receptor subfamily 0, group B, member 1 (NR0B1); GK, dystropin (DMD); and ornithine carbamoyltransferase (OTC)-cent.
Ornithine carbamoyltransferase deficiency: improved sensitivity of testing for protein tolerance in the diagnosis of heterozygotes.
liver-type arginase (ARG), ornithine carbamoyltransferase (OCT), and argininosuccinate synthase (AS), exist almost exclusively in the liver (1-3) and may serve as more specific markers of liver injury.