beta-hydroxyisovaleric aciduria

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beta-hydroxyisovaleric aciduria,

an inherited metabolic disease caused by a deficiency of an enzyme needed to metabolize the amino acid leucine. The condition results in an accumulation of leucine in the tissues, causing maple sugar odor in the urine, ketoacidosis, retardation, and muscle atrophy. See also maple syrup urine disease.

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No references found			beta-adrenergic blocking agent beta-adrenergic receptor beta-adrenergic stimulating agent Beta-agonist beta-alaninemia beta-aminopropionitrile beta-amyloid beta-amyloid protein beta-blocker beta-blocker, non-specific beta-blocker, specific Beta-blockers beta-carotene beta-cyano-l-alanine beta-endorphin beta-fetoprotein beta-fructofuranosidase beta-galactosidase beta-gamma bridge beta-glucocerebrosidase beta-glucuronidase Beta-HCG beta-hemolytic streptococci Beta-human chorionic gonadotropin beta-hydroxybutyric acid beta-hydroxyisovaleric aciduria beta-interferon beta-ketobutyric acid beta-lactam beta-lactam antibiotic beta-lactamase beta-lactamase resistance beta-lactamase-resistant antibiotics beta-lactamase-resistant penicillin beta-lipoprotein beta-lipotrophin beta-lipotropin beta-naphthylamine beta-oxidation beta-receptor beta-responsive sympathomimetic drugs beta-sitosterol beta-sitosterolemia beta-thalassemia beta-thromboglobulin Betablocker betacarotene betacism Betadine Betagan Betaherpesvirinae			beta-glycosidase beta-glycosidase complex beta-glycosidase complex beta-glycosidase complex beta-glycosidase complex Beta-HCG Beta-Hemolytic Group A Streptococci beta-hemolytic streptococci beta-hemolytic Streptococcus beta-hemolytic Streptococcus Beta-hexosaminidase Beta-hexosaminidase A Beta-hexosaminidase B Beta-human chorionic gonadotropin beta-hydroxy-beta-methylglutaryl coenzyme A beta-hydroxy-beta-methylglutaryl coenzyme A beta-hydroxy-beta-methylglutaryl coenzyme A beta-hydroxy-beta-methylglutaryl coenzyme A Beta-hydroxybutyrate Beta-hydroxybutyrate Beta-hydroxybutyrate Beta-hydroxybutyrate Beta-hydroxybutyrate beta-hydroxybutyrate dehydrogenase beta-hydroxybutyrate dehydrogenase beta-hydroxybutyrate dehydrogenase beta-hydroxybutyrate dehydrogenase Beta-Hydroxybutyrate/Acetoacetate beta-hydroxybutyric acid beta-hydroxybutyric acid beta-hydroxyisovaleric aciduria beta-interferon beta-interferon beta-interferon Beta-ionone Beta-ionone Beta-Ketoacyl Synthase-Chain Length Factor Beta-Ketoacyl-ACP Synthase I beta-ketobutyric acid beta-ketobutyric acid beta-ketobutyric acid beta-ketobutyric acid Beta-ketopropane Beta-ketopropane Beta-ketopropane Beta-ketothiolase deficiency beta-lactam beta-lactam beta-lactam Beta-lactam antibiotic Beta-lactam antibiotic Beta-lactam antibiotic Beta-lactam antibiotic Beta-lactam antibiotics Beta-lactam antibiotics Beta-lactam antibiotics Beta-lactam Ring Beta-lactam Ring Beta-lactam Ring Beta-Lactam Ring Records beta-lactamase

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