arhinencephaly

arhinencephaly

(ā″rīn-ĕn-sef′ă-lē) [ ¹an- + rhinencephalon]
Incomplete formation of the anterior cerebral hemispheres of the brain and related or neighboring structures.

arhinencephaly

congenital absence of the olfactory bulbs, tract or nerves. May be accompanied by prolonged pregnancy. Recorded in Guernsey, Simmental and Aberdeen Angus cattle.
References in periodicals archive ?
Various clinical presentations of AOS include oligohydramnios, cutis marmorata, upper limb micromelia and brachypodia, acrania, microcephaly, palatine or auricular malformations, intracranial calcifications, hydrocephaly, arhinencephaly, spina bifida, epilepsy, mental retardation, anatomic bronchial anomalies, renal abnormalities, and cardiovascular anomalies such as bicuspid aortic valve, atrial septal defect, Shone's complex, aortic valve stenosis, hypoplastic left heart syndrome, tetralogy of Fallot, double outlet right ventricle, portal hypertension and pulmonary hypertension.
Children with LWNH often have otherwise normal physical and neurologic development, however individual cases occurring along with chromosomal anomalies like mosaic trisomy of 7, 14, 18, 20 and X chromosomal mosaicism, congenital heart diseases (ventricular septal defect and tetralogy of Fallot) (12), CNS diseases (microcephaly, arhinencephaly and epilepsy) (13), psychomotor delay, deafness and brachydactyly have been mentioned in the literature.
Orbital hypertelorism, arhinencephaly and trigonocephaly.