angiokeratoma circumscriptum

angiokeratoma circumscriptum

a rare skin disorder characterized by discrete papules and nodules in small patches on the legs or on the trunk.
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Five varieties of angiokeratoma are generally recognized: i) generalized systemic type - angiokeratoma corporis diffusum (ACD); ii) bilateral form occurring on the dorsa of fingers and toes - angiokeratoma of Mibelli; iii) localized scrotal/vulval form - angiokeratoma of Fordyce; iv) solitary papular angiokeratoma; and v) multiple unilateral papular and plaque like, usually on lower limbs - angiokeratoma circumscriptum (naeviforme).
Other types of angiokeratomas include angiokeratoma of Mibelli, angiokeratoma of Fordyce, angiokeratoma circumscriptum, and angiokeratoma corporis diffusum (Fabry's disease).
Angiokeratoma circumscriptum usually present as papules that commonly coalesce to form plaques.
FINAL HISTOLOGICAL DIAGNOSIS: Angiokeratoma circumscriptum.
Localized angiokeratoma may be solitary or multiple and has been further classified into Fordyce's angiokeratoma (distributed on the genitals), Mibelli's angiokeratoma (dorsum of toes and fingers) and angiokeratoma circumscriptum naeviforme (unilateral large keratotic plaques).