aggressive angiomyxoma

aggressive angiomyxoma

locally invasive, but nonmetastasizing tumor of genital organs in young women.

Aggressive Angiomyxoma

A rare, locally aggressive, non-metastasising tumour of the vulva, vagina, pelvis and/or perineum, usually of pre-menopausal women. In the vulva, it presents as a firm, rubbery subcutaneous mass, often near Bartholin’s gland, and may be misdiagnosed as a Bartholin’s gland cyst.
Management Wide local excision without lymphadenectomy.
Prognosis Late recurrence occurs in 35–72%; no metastases have been reported.

ag·gres·sive an·gi·o·myx·o·ma

(ă-gres'iv an'jē-ō-miks-ō'mă)
Locally invasive, but nonmetastasizing tumor of genital organs in young women.
References in periodicals archive ?
The medical literature suggests that about 3 out of 10 (30%) aggressive angiomyxoma tumours will come back (recur].
Aggressive angiomyxoma mostly affects women and arises in the perineal and pelvic regions.
Aggressive angiomyxoma (AA) is a rare soft-tissue tumor that is typically found in the perineum of females of reproductive age.
The differential diagnosis might include a myxoid tumor such as myxoid neurofibroma or aggressive angiomyxoma due to the presence of myxoid, proteinaceous, or mucinous contents.
Cellular angiofibroma can also be confused with aggressive vulvo-vaginal tumours like aggressive angiomyxoma and solitary fibrous tumour (1, 5).
Aggressive angiomyxoma is a rare, myofibroblastic tumour, of pelvi-perineum of young women.
Aggressive angiomyxoma of the space of retzius: a case report.
There are 5 entities commonly accepted as myxomas: intramuscular myxoma, juxta articular myxoma, superficial angiomyxoma (or cutaneous myxoma), aggressive angiomyxoma (usually pelvic and perineal regions) and myxoma of nerve sheath (myxoid neurothekeoma).
Aggressive angiomyxoma of pelvic parts exhibits estrogen and progesterone receptor positivity.
Fallopian tube prolapse mimicking aggressive angiomyxoma.
Cutaneous angiomyxoma is to be differentially diagnosed and distinguished from other myxoidtumour including benign and low grade malignant myxoid lesions like aggressive angiomyxoma, focal cutaneous mucinosis, myxoidneurothekeomas, myxoidneurofibroma, superficial acralfibromyxoma and myxoidliposarcoma.
1] CAF share pathological features of angiomyofibroblastoma and aggressive angiomyxoma (AAM), but do not fall into either category.