retroperitoneal sarcoma

A nonspecific term for any sarcoma arising in the retroperitoneal region, which comprises 15% of all sarcomas (of 8,600 cases/year, USA).

Clinical findings
Often asymptomatic abdominal mass; average age, 50.

Prognosis
65% to 80% of cases achieve complete resection; 5-year local recurrence, ±50%; 5-year survival, ±50%.

Histological types of retroperitoneal sarcoma
• Liposarcoma—41%;
• Leiomyosarcoma—28%;
• Malignant fibrous histiocytoma (MFH)—7%;
• Fibrosarcoma—6% (MFH and fibrosarcoma are now viewed as synonyms);
• Malignant peripheral nerve sheath tumour—3%.

Mentioned in

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References in periodicals archive

Summary: Both patient and her kidney saved by operation on retroperitoneal sarcoma

Doctors remove 3.5kg kidney tumour in Dubai

Neoadjuvant radiotherapy for retroperitoneal sarcoma: a systematic review.

Dedifferentiated Liposarcoma With Myofibroblastic Differentiation

Carcinoma caecum and retroperitoneal sarcoma accounts for 4% of cases.

APPENDICULAR MASS--A PROSPECTIVE AND COMPARATIVE STUDY

The Transatlantic Retroperitoneal Sarcoma Working Group (TARPSWG) has published on 1,007 primary RPS patients treated in eight North American and European sarcoma centers from 2002 to 2011 [8, 9].

The Volume-Outcome Relationship in Retroperitoneal Soft Tissue Sarcoma: Evidence of Improved Short- and Long-Term Outcomes at High-Volume Institutions

Hannay et al., "Outcome following resection of retroperitoneal sarcoma," British Journal of Surgery, vol.

Spinal Metastasis of Well-Differentiated Liposarcoma Component in Retroperitoneal Dedifferentiated Liposarcoma Treated by Minimally Invasive Surgery

Chakraborty, "Giant myelolipoma of left adrenal gland simulating a retroperitoneal sarcoma," International Journal of Advanced Medical and Health Research, vol.

Giant Adrenal Myelolipoma in a Patient without Endocrine Disorder: A Case Report and a Review of the Literature

Magnetic resonance imaging (MRI) of the pelvis followed and confirmed the solid nature of this mass, showing that it was independent from the bowel/rectum, featuring a retroperitoneal sarcoma type of mass rather than a lymph nodal bloc (Figure 1(b)).

Retroperitoneal Solitary Fibrous Tumor: A "Patternless" Tumor

Prognostic factors in retroperitoneal sarcoma: A multi-variateanalysis of a series of 165 patients of the French Cancer Center Federation Sarcoma Group.

Tumeurs retroperitoneales primitives: profils diagnostique, therapeutique et anatomopathologique

Theoretically, the best option for retroperitoneal sarcoma is complete resection plus adjuvant therapy.

Prognostic Factors Predicting the Postoperative Survival Period Following Treatment for Primary Retroperitoneal Liposarcoma

"The role of surgical margin status in retroperitoneal sarcoma," J Surg Oncol., 98, pp.607-610.

Oncological principles in the surgical treatment of primary retroperitoneal soft tissue sarcomas

The most commonly encountered among the malignant mesenteric tumours are lymphomas followed by leiomyosarcoma.1 We present a case of huge mesenteric liposarcoma which was mistakenly labelled as a case of retroperitoneal sarcoma and the patient was being denied surgery for fear of irresectability due to its very large size.

Huge mesenteric liposarcoma