Timmermans, "Therapeutic strategy for Wunderlich syndrome
," Acta Urologica Belgica, vol.
In the Wunderlich syndrome
, the blind hemivagina is developed and filled with a large hematocolpos.
Wunderlich syndrome is a spontaneous, non-traumatic, subcapsular or perirenal hemorrhage.
Cases of Wunderlich syndrome resulting from ES are extremely rare.
As only one case of Wunderlich syndrome with primary renal ES has been previously reported, this case report is a valuable addition to the limited literature in this area.
INTRODUCTION: Congenital anomalies of the mullerian duct system can result in various urogenital anomalies and, Herlyn Werner Wunderlich syndrome
(HWW syndrome) is one such rare anomaly.
(WS) is a rare condition in which spontaneous renal hemorrhage occurs into the subcapsular and perirenal spaces.
This case report describes Wunderlich syndrome secondary to renal angiomyolipoma in a previously fit, young and healthy patient.
To the best of our knowledge, this is the first case report of Wunderlich syndrome in a young, fit patient with no significant past medical history or classic symptoms, resulting in an emergency nephrectomy.
In a review of the diagnosis and management of 7 cases of Wunderlich syndrome, Cubillana et al also found conservative management to be the most acceptable option, unless a malignant pathology could be demonstrated (14).
In conclusion, we have presented a case of Wunderlich syndrome due to rupture of a renal AML in a patient with tuberous sclerosis, which is the commonest cause reported in most series.