: Intuitiva /I (world premieres) MoEns, conductor: Miroslav Pudlak
Originally described by Hermansky and Pudlak
in 1959, (77) Hermansky-Pudlak
Syndrome (HPS) is caused by a related group of autosomal recessive disorders that are characterized by the triad of oculocutaneous albinism, bleeding diathesis due to a platelet storage pool deficiency, and lysosomal accumulation of ceroid lipofuscin.
syndrome (HPS) is an autosomal recessive disease characterized with oculocutaneous albinism and platelet aggregation disorder which was described by Hermansky and Pudlak
in 1959 (1).
WORCESTER - Lingyang Wang hovered by her scientific poster, which hung by chains from the ceiling of Abbott Bioresearch Center's cafeteria, and took occasional sips of iced tea as she explained the experiments she has conducted on mice and what they might mean for the rare genetic disease Hermansky Pudlak
z" and "LogAx(x)", such that features characteristic of these predicates are provable in a weak fragment of PA; see Kaye 1991 and Hajek and Pudlak
1993 for more details.
, who was treasurer, succeeds Smith as chief financial officer.
Albinism: Ocular and Oculocutaneous Albinism and Hermansky Pudlak
Syndrome (Richard A.
If you will allow me to strike a somewhat more personal tone than usual, I would like to share my joy at the fact that the international music fest, which eight years ago Miroslav Pudlak
, the former director of the Czech Music Information Centre, and I founded, will be on again this year.
Noteworthy too were three concerts given by the MoEns ensemble, exclusively focused on contemporary music, during which they presented new works by Jiri Kaderabek, Zdenek Bartosik, Miroslav Pudlak
and Petr Cigler.
After several changes of head of the Music Information Centre, in 1995 Miroslav Pudlak
, the current director, assumed the post on the basis of a contest.
In 1983 the young Prague composers Petr Kofrori (1955), Miroslav Pudlak
(1961) and Martin Smolka (1959) established Agon, an ensemble which in addition to their own works and compositions by their generational peers got down to performing pieces by foreign composers, mostly in thematically focused series.
It has recorded composer profile CDs of the music of Peter Graham and Miroslav Pudlak
and the anthology The End of the 20th Century in Czech Music.