Mondini dysplasia


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Mon·di·ni dys·pla·si·a

(mōn-dē'nē),
congenital anomaly of osseus and membranous otic labyrinth characterized by aplastic cochlea and deformity of the vestibule and semicircular canals with partial or complete loss of auditory and vestibular function; may be associated with dilated vestibular aqueduct and spontaneous cerebrospinal fluid otorrhea resulting in meningitis.
See also: Mondini hearing impairment.

Mon·di·ni dys·pla·sia

(mon-dē'nē' dis-plā'zē-ă)
Congenital anomaly of osseus and membranous labyrinth characterized by aplastic cochlea, and deformity of the vestibule and semicircular canals with partial or complete loss of auditory and vestibular function; may be associated with spontaneous cerebrospinal fluid otorrhoea resulting in meningitis.
References in periodicals archive ?
Like other temporal bone defects or other congenital anatomic causes of recurrent meningitis; in Mondini dysplasia the CSF leaks into the middle ear through a deficient foramen ovale, which is a risk factor for recurrent pneumococcal infections (8).
The use of cochlear implantation to treat patients with inner ear malformations such as Mondini dysplasia has been increasingly successful the world over," he said.
Spontaneous cerebrospinal fluid otorrhea in association with a congenital defect of the cochlear aqueduct and Mondini dysplasia.