Marie-Strümpell disease


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Related to Marie-Strümpell disease: ankylosing spondylitis, Bamboo spine, Spondylitis ankylopoetica, Bechterew's, Bechterew disease

spondylitis

 [spon″dĭ-li´tis]
inflammation of the vertebrae, usually a serious and chronic disorder. It may be associated with tuberculosis of the bones, in which case it is called pott's disease. The vertebrae become eroded and collapse, causing kyphosis. Spondylitis may also be associated with other infectious diseases, such as brucellosis, in which the intervertebral disks and the vertebrae are affected and sometimes destroyed; this is one cause of ankylosing spondylitis, a particularly serious variety.
ankylosing spondylitis (Bekhterev's spondylitis) a form of rheumatoid arthritis that affects the spine, characterized by inflammation of the facet joints and inflammatory changes of the stabilizing ligaments of the spine (enthesopathy). It affects males almost exclusively. There is stiffening of spinal joints and ligaments, so that movement becomes increasingly painful and difficult. When it runs its full course, it results in bony ankylosis of the vertebral joints, which may extend to the ribs and limit the flexibility of the rib cage, so that breathing is impaired. Called also Marie-Strümpell disease or spondylitis and rheumatoid spondylitis.
Typical posture of patient with ankylosing spondylitis. From Copstead and Banasik, 2000.
Kümmell's spondylitis Kümmell's disease.
Marie-Strümpell spondylitis ankylosing spondylitis.
post-traumatic spondylitis Kümmell's disease.
rheumatoid spondylitis ankylosing spondylitis.

an·ky·los·ing spon·dy·li·tis

[MIM*106300]
arthritis of the spine, resembling rheumatoid arthritis, which may progress to bony ankylosis with ossification of the anterior and posterior longitudinal ligaments; the disease is more common in males, often with the rheumatoid factor absent and the HLA antigen present. There is a striking association with the B27 tissue type and the strong familial aggregation suggests an important genetic factor, perhaps inherited as an autosomal dominant [MIM*106300]; the mechanism, however, remains obscure.

Marie-Strümpell arthritis, Marie-Strümpell disease

Marie-Strümpell disease

(1) Ankylosing spondylitis, see there.
(2) Acquired infantile hemiplegia, see there.

Marie,

Pierre, French neurologist, 1853-1940.
Bamberger-Marie disease - Synonym(s): Bamberger-Marie syndrome
Bamberger-Marie syndrome - see under Bamberger, Eugen
Brissaud-Marie syndrome - see under Brissaud
Charcot-Marie-Tooth disease - see under Charcot
Debré-Marie syndrome - see under Debré
Foix-Cavany-Marie syndrome - see under Foix
Marie ataxia - obsolete term for a variety of non-Friedreich hereditary ataxias.
Marie-Leri syndrome - swelling of deformed joints.
Marie-Sainton syndrome - excessive head development. Synonym(s): cleidocranial dysplasia; cleidocranial dysostosis
Marie-Strümpell disease - Synonym(s): Strümpell-Marie disease
Marie I syndrome - Synonym(s): Menzel syndrome
Marie II syndrome - endocrine and neurologic disorders.
Nonne-Marie syndrome - Synonym(s): Menzel syndrome
Strümpell-Marie disease - see under Strümpell

Strümpell,

Ernst Adolf von, German physician, 1853-1925.
Fleischer-Strümpell ring - Synonym(s): Kayser-Fleischer ring
Marie-Strümpell disease - Synonym(s): Strümpell-Marie disease
Strümpell disease - arthritis and osteitis deformans involving the spinal column. Synonym(s): acute epidemic leukoencephalitis; spondylitis deformans
Strümpell-Marie disease - arthritis of the spine, resembling rheumatoid arthritis, that may progress to bony ankylosis. Synonym(s): ankylosing spondylitis; Marie-Strümpell disease
Strümpell phenomenon - dorsal flexion of the great toe in a paralyzed limb when the limb is drawn up against the body, flexing knee and hip. Synonym(s): tibial phenomenon
Strümpell reflex - stroking the abdomen or thigh causes flexion of the leg and adduction of the foot.
Strümpell-Westphal disease - Synonym(s): Wilson disease
Westphal-Strümpell pseudosclerosis - Synonym(s): Wilson disease
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