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Malformation consisting of a cranial defect at the occiput, with the brain exposed; often in combination with a cervical rachischisis and retroflexion.
[G. inion, back of the head, + enkephalos, brain]
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References in periodicals archive ?
The most prevalent are spina bifida and anencephaly and also include encephalocele, craniorachischisis, and iniencephaly (Kondo, Kamihira, & Ozawa, 2009).
INTRODUCTION: Iniencephaly is a rare birth defect having retroflexion of the head combined with severe distortion of the spine.
Most of iniencephalic babies are stillborn or die soon after birth (2, 9); however the milder forms of iniencephaly cases are not fatal.
Here we present a rare case of iniencephaly clausus with review of literature.
DISCUSSION: INIENCEPHALY is a rare neural tube defect that results in deficiency of occiput in the region of foramen magnum, spina bifida of considerable extent (up to spinal rachischisis) & cervicothoracic spinal retroflexion (3, 5).
Se realizo una busqueda en la bases de dato Medline via PubMed con criterio de busqueda avanzada, con la palabra clave iniencephaly en titulo y/o abstract.
Major diagnostic and pathological features of iniencephaly based on twenty-four cases.
Iniencephaly and associated anomalies: an embryo pathogenesis analysis.
Prenatal diagnosis in three cases of iniencephaly with unusual postmortem findings.
Transvaginal sonographic diagnosis of iniencephaly apertus and craniorachischisis at 9 weeks' gestation.
Congenital malformations associated with anencephaly and iniencephaly.
In another case cited by Walker (1974) a woman took meclizine and another antiemetic and had a child with iniencephaly and spina bifida.