West Syndrome
(redirected from Infantile myoclonic encephalopathy)

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West Syndrome

An early onset condition characterised by a triad:
(1) Infantile spasms,
(2) Interictal EEG pattern termed hypsarrhythmia, and
(3) Mental retardation. Per the international classification, the diagnosis can be made in the presence of two of the three symptoms. The frequent onset of West syndrome in infancy suggests that CNS immaturity may play a key role in its pathogenesis. The clinical response to ACTH and glucocorticoids may be linked to suppression of corticotropin-releasing hormone production

West syndrome

Massive myoclonus Neurology An occasionally X-linked condition characterized by infantile spasms–seizures and 2º generalized epilepsy, hypsarrhythmia, encephalopathy with mental retardation and arrested psychomotor development, ± with immune dysfunction and death at an early age due to bronchopneumonia. See Salaam convulsions.

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Infantile Spasm salaam convulsion seizure syndrome			infant of diabetic mother infant seat Infanticide infantile infantile acrodermatitis infantile acropustulosis infantile agranulocytosis infantile amnesia infantile arteritis infantile autism infantile celiac disease infantile cerebral ataxic paralysis infantile cerebral sphingolipidosis infantile cirrhosis infantile colic infantile cortical hyperostosis infantile digital fibromatosis infantile dwarf infantile eczema infantile encephalitis infantile fibromatosis infantile fibrosarcoma infantile hemiplegia infantile hydrocele infantile muscular atrophy Infantile myoclonic encephalopathy infantile myofibromatosis infantile neuroaxonal dystrophy infantile osteomalacia infantile paralysis infantile pellagra infantile poliomyelitis infantile polyarteritis infantile progressive spinal muscular atrophy infantile purulent conjunctivitis infantile scurvy infantile sexuality Infantile Spasm infantile spasms infantile spinal muscular atrophy infantile spinal paralysis infantile uterus infantilism infantophagia infarct infarct extension infarct-avid scintigraphy infarctectomy infarction Infasurf infect			Infantile genetic agranulocytosis Infantile genetic agranulocytosis Infantile genetic agranulocytosis infantile genitalia infantile giantism infantile giantism infantile giantism infantile glaucoma infantile glaucoma infantile glaucoma infantile hemiplegia infantile hydrocele Infantile Hypercalcaemia/Williams-Beuren Syndrome Infantile hypercalcemia Infantile hypercalcemia infantile hypertrophic gastric stenosis infantile hypertrophic gastric stenosis infantile hypertrophic gastric stenosis Infantile Hypertrophic Pyloric Stenosis Infantile Hypotonia Infantile Hypotonia Infantile Hypotonia Infantile Idiopathic Nephrotic Syndrome infantile lobar emphysema infantile lobar emphysema infantile lobar emphysema infantile massive s infantile massive s infantile massive s infantile muscular atrophy Infantile myoclonic encephalopathy infantile myofibromatosis infantile neuroaxonal dystrophy infantile neuroaxonal dystrophy infantile neuroaxonal dystrophy Infantile Neuronal Ceroid Lipofuscinosis infantile osteomalacia infantile paralysis infantile paralysis infantile paralysis infantile paralysis infantile pellagra infantile pelvis infantile pelvis infantile pelvis Infantile Perianal Pyramidal Protrusion infantile poliomyelitis Infantile polyarteritis Infantile polyarteritis Infantile Polyarthritis Infantile Polycystic Kidney Disease Infantile polycystic kidneys Infantile polycystic kidneys infantile progressive spinal muscular atrophy infantile purulent conjunctivitis infantile pustular dermatosis infantile pustular dermatosis infantile pustular dermatosis Infantile Refractory Grand Mal Syndrome Infantile Refsum disease Infantile Refsum disease

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West Syndrome (redirected from Infantile myoclonic encephalopathy)

West Syndrome
(redirected from Infantile myoclonic encephalopathy)