hereditary spherocytosis

spherocytosis /sphe·ro·cy·to·sis/ (sfēr″o-si-to´sis) the presence of spherocytes in the blood.

hereditary spherocytosis a congenital hereditary form of hemolytic anemia characterized by spherocytosis, abnormal fragility of erythrocytes, jaundice, and splenomegaly.

A congenital defect in the cell membrane of red blood cells resulting in thickened, fragile red blood cells that are susceptible to spontaneous hemolysis and marked by chronic anemia, reticulocytosis, mild jaundice, and fever and abdominal pain. Also called chronic acholuric jaundice, chronic familial jaundice, congenital hemolytic anemia, congenital hemolytic jaundice, spherocytic anemia.

Hereditary spherocytosis (HS)

A blood disorder in which the red blood cells are relatively fragile and are damaged or destroyed when they pass through the spleen. Splenectomy is the only treatment for HS.

Mentioned in: Splenectomy

hereditary spherocytosis.

See spherocytic anemia.

spherocytosis [sfe″ro-si-to´sis]

the presence of spherocytes in the blood.

hereditary spherocytosis a congenital hereditary form of hemolytic anemia characterized by spherocytosis, abnormal fragility of erythrocytes, jaundice, and splenomegaly.

hereditary spherocytosis

Spherocytosis Neonatology An AD condition characterized by ↑ osmotic fragility of red cells, autohemolysis, splenomegaly and mild anemia partially corrected by splenectomy; HS is linked to a defect in a 28 kD RBC membrane protein Management Splenectomy. Cf Spherocytosis.

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acholuric jaundice chronic acholuric jaundice chronic familial jaundice congenital hemolytic anemia congenital hemolytic jaundice Fish Mouth Vertebrae fish vertebrae hemolytic anemia hemolytic jaundice hepatocellular jaundice hs jaundice mechanical jaundice monoclonal immunoglobulin nuclear jaundice obstructive jaundice osmotic fragility Pink Test retention jaundice	hereditary spherocytosis or RBC coated with antibodies) is not able to transverse the sinusoidal network and is then phagocytosed and destroyed by macrophages. Drug-induced haemolytic anaemia by Sinxadi, Phumla; Maartens, Gary / CME: Your SA Journal of CPD A A peripheral blood osmotic fragility test has traditionally been considered important in the workup of hereditary spherocytosis (HS). Utility of osmotic fragility test by Baer, Daniel M. / Medical Laboratory Observer Partial splenic embolization in a child with hereditary spherocytosis. Severe thrombocytopenia due to hypersplenism successfully treated ... by Pandya, Prashant / Southern Medical Journal	hereditary elliptocytosis hereditary enamel hypoplasia hereditary essential tremor hereditary fructose intolerance hereditary hemochromatosis hereditary hemorrhagic telangiectasia hereditary hypertrophic neuropathy hereditary hyperuricemia hereditary lymphedema hereditary motor & sensory neuropathy hereditary multiple exostoses hereditary mutation hereditary neoplasia hereditary nephritis hereditary neuralgic amyotrophy hereditary nonpolyposis colon cancer Hereditary Opalescent Dentin hereditary oral disease hereditary osteoonychodysplasia hereditary persistence of fetal hemoglobin hereditary preneoplasia hereditary progressive arthro-ophthalmopathy hereditary protoporphyria hereditary renal adysplasia hereditary sensory neuropathy hereditary spherocytosis hereditary spinal ataxia hereditary thrombophilia hereditary tyrosinemia heredity heredo- heredofamilial heredomacular degeneration Hereford Herellea Hering's law of cure Hering's nerve Hering-Breuer reflex Hering-Breuer reflexes Hering-Hermann grid heritability heritable Heritage Pork Hermann's tortoise Hermansky-Pudlak syndrome hermaphrodism hermaphrodite hermaphroditism hermeneutic circle Hermes' wing hermetic	Hereditary Resistance to Activated Protein C hereditary sensory and autonomic neuropathy hereditary sensory and autonomic neuropathy hereditary sensory and autonomic neuropathy hereditary sensory and autonomic neuropathy Hereditary Sensory and Autonomic Neuropathy Type I hereditary sensory and autonomic neuropathy type IV Hereditary Sensory and Autonomic Neuropathy with Anosmia Hereditary Sensory and Autonomic Neuropathy, Type III Hereditary Sensory Motor Neuropathy hereditary sensory neuropathy hereditary sensory neuropathy hereditary sensory neuropathy hereditary sensory neuropathy Hereditary Sensory Neuropathy type 1 Hereditary sensory neuropathy type I hereditary sensory radicular neuropathy hereditary sensory radicular neuropathy hereditary sensory radicular neuropathy hereditary sideroachrestic anemia hereditary sideroachrestic anemia hereditary sideroachrestic anemia hereditary sideroblastic anemia hereditary sideroblastic anemia hereditary sideroblastic anemia Hereditary Site-Specific Colonic Cancer Hereditary Site-Specific Ovarian Cancer Hereditary Society Blue Book Hereditary spastic paraplegia hereditary spastic paraplegia with a thin corpus callosum hereditary spherocytosis hereditary spinal ataxia hereditary spinal ataxia hereditary spinal ataxia hereditary spinal muscular atrophy hereditary spinal muscular atrophy hereditary spinal muscular atrophy Hereditary Stiff Person Syndrome Hereditary Stiff-Man Syndrome Hereditary stomatocytosis Hereditary Stress-Induced Arterial Hypertension Hereditary Stress-Induced Hypertensive Rats Hereditary succession hereditary thrombopathias hereditary thrombopathias hereditary thrombopathias hereditary thrombopathias hereditary thrombophilia Hereditary Transthyretin hereditary tyrosinemia Hereditary Tyrosinemia 1 Hereditary Tyrosinemia Type 1 Hereditary Tyrosinemia type I Hereditary Tyrosinemias Hereditary Tyrosinemias Hereditary Tyrosinemias Hereditary urogenital adysplasia Hereditary Vitamin D Resistant Rickets hereditary zinc deficiency hereditary zinc deficiency hereditary zinc deficiency

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acholuric jaundice
chronic acholuric jaundice
chronic familial jaundice
congenital hemolytic anemia
congenital hemolytic jaundice
Fish Mouth Vertebrae
fish vertebrae
hemolytic anemia
hemolytic jaundice
hepatocellular jaundice
hs
jaundice
mechanical jaundice
monoclonal immunoglobulin
nuclear jaundice
obstructive jaundice
osmotic fragility
Pink Test
retention jaundice

hereditary spherocytosis or RBC coated with antibodies) is not able to transverse the sinusoidal network and is then phagocytosed and destroyed by macrophages.

Drug-induced haemolytic anaemia by Sinxadi, Phumla; Maartens, Gary / CME: Your SA Journal of CPD

A A peripheral blood osmotic fragility test has traditionally been considered important in the workup of hereditary spherocytosis (HS).

Utility of osmotic fragility test by Baer, Daniel M. / Medical Laboratory Observer

Partial splenic embolization in a child with hereditary spherocytosis.

Severe thrombocytopenia due to hypersplenism successfully treated ... by Pandya, Prashant / Southern Medical Journal

hereditary elliptocytosis

hereditary enamel hypoplasia

hereditary essential tremor

hereditary fructose intolerance

hereditary hemochromatosis

hereditary hemorrhagic telangiectasia

hereditary hypertrophic neuropathy