hereditary angioedema

angioedema /an·gio·ede·ma/ (-ĕ-de´mah) a vascular reaction involving the deep dermis or subcutaneous or submucosal tissues, representing localized edema caused by dilatation and increased permeability of the capillaries, and characterized by the development of giant wheals.

hereditary angioedema an autosomal dominant disorder of C1 inhibitor (C1 INH), which causes uncontrolled activation of the classical complement pathway, manifested as recurrent episodes of edema of the skin and upper respiratory and gastrointestinal tracts with increased levels of several vasoactive mediators of anaphylaxis. It may be mediated by such factors as minor trauma, sudden changes in environmental temperature, and sudden emotional stress.

Hereditary angioedema

A complement deficiency characterized by lymphatic vessel blockages that cause temporary swelling (edema) of areas of the skin, mucous membranes, and, sometimes, internal organs.

Mentioned in: Complement Deficiencies

hereditary angioedema,

an inherited autosomal-dominant disorder characterized by the episodic appearance of nonpitting edema involving any part of the body, including mucosal surfaces. The attacks last 48 to 72 hours and can be life-threatening if edema obstructs the airway.

angioedema [an″je-o-ĕ-de´mah]

a localized edematous reaction of the deep dermis or subcutaneous or submucosal tissues appearing as giant wheals; urticaria is the same physiologic reaction occurring in the superficial portions of the dermis.

hereditary angioedema an autosomal dominant disorder of the complement system manifested as recurrent episodes of edema of the skin, upper respiratory tract, and gastrointestinal tract. It may be mediated by such factors as minor trauma, sudden changes in environmental temperature, and sudden emotional stress. adj., adj angioede´matous.

angioedema

a condition characterized by the sudden and temporary appearance of large areas of painless swelling in the subcutaneous tissue or submucosa, with or without pruritus. Caused by immunological reactions, usually immediate type hypersensitivities. Sometimes referred to as angioneurotic edema.

hereditary angioedema

in humans, the periodic occurrence of angioedema caused by a deficiency of the complement regulatory protein.

Mentioned in	?		References in periodicals archive	?		Medical browser	?		Full browser	?
angioedema angiogenesis inhibitor aromatase inhibitors C1 INH carbonic anhydrase inhibitor cholinesterase inhibitor Complement Deficiencies COX-2 inhibitors danazol Danocrine ethoxzolamide gastric acid pump inhibitor hereditary angioneurotic edema HIV protease inhibitor indinavir inhibitor MAO inhibitor MAOI monoamine oxidase inhibitor	Dewald G, Bork K: Missense mutations in the coagulation factor XII gene in hereditary angioedema with normal C1 inhibitor. A Family with hereditary angioedema having been followed as familial ... by Sarici, Gulben; Koca, Rafet; Tekin, Nilgun Solak; Altinyazar, Hilmi Cevdet / Archives of the Turkish Dermatology and Venerology Hereditary angioedema is a rare but serious condition affecting the immune system that is passed down through families. I never know when it will happen next; Swelling attacks from rare ... by South Wales Echo (Cardiff, Wales) Key Words: bradykinin, erythema marginatum, hereditary angioedema ********** Hereditary Cl-esterase inhibitor deficiency is accompanied by two dermal manifestations, angioedema and erythema marginatum. Erythema marginatum and hereditary angioedema by Posey, Delma / Southern Medical Journal	Herbal Tea herbalism Herbalism, Traditional Chinese Herbalism, Western herbalist herbalista Herbert screw Herbert's operation herbicide herbicide poisoning herbivore herbivorous herbolaria herbology Herbst appliance Herceptin HERCULES Hercules Nd:YAG Laser herd Herd Immunity herd instinct herding hereditability hereditary hereditary amyloidosis hereditary angioedema hereditary angioneurotic edema hereditary ataxia hereditary benign intraepithelial dyskeratosis hereditary brown enamel hereditary cancer syndrome hereditary cerebellar ataxia hereditary cerebral hemorrhage with amyloidosis, Dutch type hereditary cerebral leukodystrophy hereditary chorea hereditary coproporphyria hereditary deforming chondroplasia hereditary disorder hereditary elliptocytosis hereditary enamel hypoplasia hereditary essential tremor hereditary fructose intolerance hereditary hemochromatosis hereditary hemorrhagic telangiectasia hereditary hypertrophic neuropathy hereditary hyperuricemia hereditary lymphedema hereditary motor & sensory neuropathy hereditary multiple exostoses hereditary mutation hereditary neoplasia	hereditarianism Hereditarians hereditarily hereditarily hereditarily hereditarily hereditariness hereditariness hereditariness hereditariness hereditarius hereditary hereditary hereditary hereditary Hereditary Acromelalgia Hereditary Acromelalgia Hereditary Acromelalgia Hereditary Adrenocortical Unresponsiveness to ACTH hereditary adult-onset leukodystrophy hereditary adult-onset leukodystrophy hereditary allergy hereditary allergy hereditary allergy hereditary amblyopia with quadriplegia hereditary amblyopia with quadriplegia hereditary amblyopia with quadriplegia Hereditary amyloidosis Hereditary amyloidosis Hereditary amyloidosis hereditary angioedema hereditary angioneurotic edema hereditary angioneurotic edema hereditary angioneurotic edema hereditary angioneurotic edema Hereditary Arterial Hypertension Induced by Stress Hereditary ataxia Hereditary ataxia Hereditary ataxia Hereditary ataxia hereditary benign intraepithelial dyskeratosis Hereditary Breast and Ovarian Cancer hereditary brown enamel hereditary brown teeth hereditary brown teeth hereditary brown teeth hereditary brown teeth Hereditary Bundle Branch System Defect Hereditary Cancer in Clinical Practice hereditary cancer syndrome Hereditary Canine Spinal Muscular Atrophy Hereditary Captaincies Hereditary central nervous system demyelinating diseases Hereditary central nervous system demyelinating diseases hereditary cerebellar ataxia hereditary cerebellar ataxia Hereditary Cerebral Hemorrhage with Amyloidosis Hereditary Cerebral Hemorrhage with Amyloidosis of the Dutch-Type Hereditary Cerebral Hemorrhage with Amyloidosis, Dutch Type Hereditary Cerebral Hemorrhage with Amyloidosis-Dutch Type Hereditary Cerebral Hemorrhage with Amyloidosis-Icelandic type

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angioedema
angiogenesis inhibitor
aromatase inhibitors
C1 INH
carbonic anhydrase inhibitor
cholinesterase inhibitor
Complement Deficiencies
COX-2 inhibitors
danazol
Danocrine
ethoxzolamide
gastric acid pump inhibitor
hereditary angioneurotic edema
HIV protease inhibitor
indinavir
inhibitor
MAO inhibitor
MAOI
monoamine oxidase inhibitor

Dewald G, Bork K: Missense mutations in the coagulation factor XII gene in hereditary angioedema with normal C1 inhibitor.

A Family with hereditary angioedema having been followed as familial ... by Sarici, Gulben; Koca, Rafet; Tekin, Nilgun Solak; Altinyazar, Hilmi Cevdet / Archives of the Turkish Dermatology and Venerology

Hereditary angioedema is a rare but serious condition affecting the immune system that is passed down through families.

I never know when it will happen next; Swelling attacks from rare ... by South Wales Echo (Cardiff, Wales)

Key Words: bradykinin, erythema marginatum, hereditary angioedema ********** Hereditary Cl-esterase inhibitor deficiency is accompanied by two dermal manifestations, angioedema and erythema marginatum.

Erythema marginatum and hereditary angioedema by Posey, Delma / Southern Medical Journal

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