Hereditary Fibrous Dysplasia of the Jaws

cherubism /cher·ub·ism/ (cher´ub-izm) hereditary progressive bilateral swelling at the angle of the mandible, and sometimes the entire jaw, giving a cherubic look to the face, in some cases enhanced by upturning of the eyes.

cher·ub·ism (ch

-b

A hereditary disease marked by an enlargement of the jawbones in young children, producing a cherublike facial appearance.

cherubism

[cher′əbiz′əm]

Etymology: Heb, kerubh

an abnormal hereditary condition characterized by progressive bilateral swelling at the angle of the mandible, especially in children. In some cases of cherubism, the entire jaw swells and the eyes turn up, enhancing the cherubic facial appearance. The condition tends to regress during adult life.

Cherubism

An autosomal dominant [MIM 118400] condition, with 100% penetration in males who have a cherub-like physiognomy, that may be first recognised by age 5, when a child is obviously not losing the ‘baby fat’ in the face

cherubism [cher´oo͡-bizm]

hereditary and progressive bilateral swelling at the angle of the mandible, sometimes involving the entire jaw, imparting a cherubic look to the face, in some cases enhanced by upturning of the eyes.

cherubism,

n hereditary condition that causes the mandible to grow excessively; in some cases the eyes are also upturned, increasing the cherubic look on the face.

cherubism (familial intraosseous swelling) (cher´

biz´

m),

n 1. a fibroosseous disease of the jaws of genetic nature. The swollen jaws and raised eyes give a cherubic appearance; multiple radiolucencies are evident on radiographic examination.
2. a familial form of fibrous dysplasia characterized by unilateral or, more often, bilateral swelling of the jaws in children. See also dysplasia, fibrous.

Cherubism.

cherubism

Familial intraosseous fibrous swelling of jaws An AD condition, 100% penetration in ♂ with a cherub-like physiognomy, first recognized by age 5 Clinical Puffed-out cheeks, agenesis of permanent teeth, dental dysgenesis, exophthalmos, progressive, bilateral soap-bubble expansile lesions of bone, at the mandibular angle, submandibular lymphadenopathy

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familial intraosseous fibrous swelling of the jaws Soap Bubble swelling	HERCULES Hercules Nd:YAG Laser herd Herd Immunity herd instinct herding hereditability hereditary hereditary amyloidosis hereditary angioedema hereditary angioneurotic edema hereditary ataxia hereditary benign intraepithelial dyskeratosis hereditary brown enamel hereditary cancer syndrome hereditary cerebellar ataxia hereditary cerebral hemorrhage with amyloidosis, Dutch type hereditary cerebral leukodystrophy hereditary chorea hereditary coproporphyria hereditary deforming chondroplasia hereditary disorder hereditary elliptocytosis hereditary enamel hypoplasia hereditary essential tremor Hereditary Fibrous Dysplasia of the Jaws hereditary fructose intolerance hereditary hemochromatosis hereditary hemorrhagic telangiectasia hereditary hypertrophic neuropathy hereditary hyperuricemia hereditary lymphedema hereditary motor & sensory neuropathy hereditary multiple exostoses hereditary mutation hereditary neoplasia hereditary nephritis hereditary neuralgic amyotrophy hereditary nonpolyposis colon cancer Hereditary Opalescent Dentin hereditary oral disease hereditary osteoonychodysplasia hereditary persistence of fetal hemoglobin hereditary preneoplasia hereditary progressive arthro-ophthalmopathy hereditary protoporphyria hereditary renal adysplasia hereditary sensory neuropathy hereditary spherocytosis hereditary spinal ataxia hereditary thrombophilia	hereditary disease hereditary disease hereditary disease Hereditary Disease Array Group Hereditary Disease Foundation Hereditary diseases Hereditary diseases Hereditary diseases Hereditary disorder Hereditary disorder Hereditary Dysphasic Disinhibition Dementia Hereditary Dysphasic Disinhibition Dementia 2 Hereditary Dysplastic Nevus Syndrome Hereditary elliptocytosis Hereditary elliptocytosis Hereditary elliptocytosis hereditary enamel hypocalcification hereditary enamel hypocalcification hereditary enamel hypoplasia hereditary enmity Hereditary Equine Regional Dermal Asthenia Hereditary Equine Regional Dermal Asthenia Hereditary Erythrocytosis Hereditary erythropoietic porphyria Hereditary erythropoietic porphyria Hereditary erythropoietic porphyria hereditary essential tremor Hereditary Expansile Polyostotic Osteolytic Dysplasia Hereditary Factors Theory Hereditary Feudal Lease Hereditary Fibrous Dysplasia of the Jaws Hereditary Form of Benign Prostatic Hyperplasia Hereditary Forms of Inclusion Body Myopathy Hereditary fructose intolerance Hereditary fructose intolerance Hereditary fructose intolerance Hereditary fructose intolerance Hereditary Gastric Cancer Syndrome Hereditary Giant Platelet Syndrome Hereditary Gingival Fibromatosis hereditary gingival fibrosis hereditary gingival fibrosis hereditary gingival fibrosis Hereditary haemorrhagic telangiectasia Hereditary haemorrhagic telangiectasia Hereditary haemorrhagic telangiectasia type 1 Hereditary hearing disorder Hereditary hearing disorder Hereditary Hearing Impairment Hereditary Hearing Impairment Resource Registry Hereditary hearing loss Hereditary hearing loss Hereditary hemochromatosis Hereditary hemochromatosis hereditary hemorrhagic telangiectasia hereditary hemorrhagic telangiectasia hereditary hemorrhagic telangiectasia hereditary hemorrhagic telangiectasia Hereditary Hemorrhagic Telangiectasia Foundation International Hereditary Hemorrhagic Telangiectasia type 2 Hereditary hemorrhagic teleangiectasia

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familial intraosseous fibrous swelling of the jaws
Soap Bubble
swelling

HERCULES

Hercules Nd:YAG Laser