autoimmune lymphoproliferative syndrome(redirected from FAS-related autoimmune lymphoproliferative syndrome)
autoimmune lymphoproliferative syndromeA condition caused by defective lymphocyte homeostasis and characterised by:
• Non-malignant lymphoproliferation (lymphadenopathy, hepatosplenomegaly with or without hypersplenism) that often improves with age;
• Autoimmune disease, mostly directed toward peripheral blood cells; and
• Lifelong increased risk of Hodgkin and non-Hodgkin lymphoma.