extramammary Paget's disease

extramammary Paget's disease

[-mam′ərē]

Etymology: L, extra, outside, mamma, breast; James Paget, English surgeon, 1814-1899; L, dis + Fr, aise, ease

a gradually spreading red, scaly, and crusted lesion resembling that of Paget's disease but not occurring on the breast. A common area is the vulva. The lesions give rise to carcinoma in approximately 50% of the cases.

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extramammary Paget's disease

 A lesion similar to Paget's disease of breast, less often linked to underlying malignancy; the condition arises from skin adnexae, visceral malignancy or rarely, de novo, in scrotum, perineum, labia majora; cells are more often mucin-positive than in Paget's disease of breast