Dandy-Walker syndrome

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Dandy-Walker syndrome

 [dan´de-wawk´er]
congenital hydrocephalus due to obstruction of the foramina of Magendie and Luschka.

Dan·dy-Walk·er syn·drome

(dan'dē wah'kĕr), [MIM*220200]
developmental anomaly of the fourth ventricle associated with atresia of the foramina of Luschka and Magendie that results in cerebellar hypoplasia, hydrocephalus, and posterior fossa cyst formation.

Dan·dy-Walk·er syn·drome

(dan'dē waw'kĕr sin'drōm)
Developmental anomaly of the fourth ventricle associated with atresia of the foramina of Luschka and Magendie that results in cerebellar hypoplasia, hydrocephalus, and posterior fossa cyst formation.

Dandy,

Walter Edward, U.S. surgeon, 1886-1946.
Dandy ventriculostomy
Dandy clamp
Dandy forceps
Dandy hemostat
Dandy nerve hook
Dandy neurosurgical scissors
Dandy operation
Dandy suction tube
Dandy-Walker syndrome - developmental anomaly of the fourth ventricle associated with atresia of the foramina of Luschka and Magendie that results in cerebellar hypoplasia, hydrocephalus, and posterior fossa cyst formation.

Walker,

Arthur Earl, U.S. neurologist, 1907–
Dandy-Walker syndrome - see under Dandy
Walker tractotomy - a mesencephalic spinothalamic tractotomy.
Walker-Warburg syndrome - a congenital disorder, usually fatal before age one.

Dandy-Walker syndrome

congenital hydrocephalus due to obstruction of the foramina of Magendie and Luschka. A deformity in humans also recorded in dogs and sheep. Called also Dandy-Walker malformation.
References in periodicals archive ?
Lennox-Gastant syndrome and Dandy-Walker malformation
My 11-year-old daughter, Lindsey Marie, has Lennox-Gastaut syndrome (an atypical type of epilepsy which is characterized by numerous daily uncontrollable seizures); and Dandy-Walker malformation (a malformation of several key openings in the brain which leads to an accumulation of fluid).
Failure of these neural proliferation processes results in midline supratentorial anomalies such as holoprosencephaly, agenesis of the corpus callosum, pituitary maldevelopment and posterior fossa malformations such as Dandy-Walker malformation, cerebellar hypoplasia and rhombencephalosynapsis.
Further analysis showed that cerebellar abnormalities that proved the involvement of FOXC1 in Dandy-Walker malformation.
The gene called FOXC1 is believed to contribute to Dandy-Walker malformation (DWM), a brain defect that occurs in 1 of every 5,000 births.
Lennox-Gastaut syndrome and Dandy-Walker malformation
A 3-month-old male infant was initially diagnosed with a Dandy-Walker malformation based on head CT findings.
A prominent cisterna magna is noted, but there are no other findings to suggest a Dandy-Walker malformation.
Congenital hydrocephalus' is often associated with myelomeningocele, but may also be caused by aqueduct stenosis, Dandy-Walker malformation, intrauterine infection, germinal matrix haemorrhage and rarely by an X-linked inherited disorder.
One of these had a severe Dandy-Walker malformation, and the pregnancy was terminated medically.
1) confirmed the Dandy-Walker malformation on the basis of an absent vermis, cystic dilatation of the fourth ventricle, an enlarged posterior fossa, upward displacement of the torcula and splayed hypoplastic cerebellar hemispheres.