cystic adenomatoid malformation


Also found in: Acronyms.

cys·tic ad·e·no·ma·toid mal·for·ma·tion

a rare developmental lung-bud abnormality that results in stillbirth, acute progressive respiratory disease of newborns, or protracted childhood pneumonias; combines features of a hamartoma, dysplastic growth, and tumorous growth. Three types have been described, based chiefly on cyst diameters: Type I: up to 10 cm; Type II: less than 1.2 cm; and Type III: less than 0.5 cm.
References in periodicals archive ?
In the first thorax CT taken, an appearance in line with cystic adenomatoid malformation and consolidation was present in left lung upper lobe (Figure 2).
Stocker JT, Drake RM: Congenital cystic adenomatoid malformation of the lung.
Atypical goblet cell hyperplasia in congenital cystic adenomatoid malformation as a possible preneoplasia for pulmonary adenocarcinoma in childhood: a genetic analysis.
Congenital cystic adenomatoid malformation is an embrionic developmental disorder characterized by cystic enlargement and overgrowth of terminal bronchioles which are surrounded by various epithelial cells.
Congenital cystic adenomatoid malformations (CCAM) are the most commonly diagnosed prenatal lung malformations and account for approximately 30% to 40% of all congenital anomalies.
Of four cases with cardiac malposition due to extracardiac anomalies, one had congenital diaphragmatic hernia and other had cystic adenomatoid malformation.
In congenital cystic adenomatoid malformation, an absence of bronchial cartilage leads to air trapping.
DISCUSSION: Congenital cystic adenomatoid malformation is an uncommon congenital malformation of lung, arising from excessive disorganized proliferation of terminal, tubular bronchial structures excluding alveoli.
Mucinous cells in type 1 pulmonary congenital cystic adenomatoid malformation as mucinous bronchioloalveolar carcinoma precursors.
2) It presents as an echogenic lung mass during the prenatal period, and other differential diagnoses include cystic adenomatoid malformation (CAM), sequestrated lung, and tracheal or bronchial atresia.
They include congenital cystic adenomatoid malformation (CCAM), congenital diaphragmatic hernia (CDH), bronchopulmonary sequestration (BPS), congenital hydrothorax, and congenital lobar emphysema.
The early images may be confusing and may lead to a spurious diagnosis of cystic adenomatoid malformation or of other pulmonary masses, as the emphysematous lobe is frequently filled with amniotic fluid that has not yet cleared.