coproporphyrinogen oxidase

(redirected from Coproporphyrinogen III oxidase)
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cop·ro·por·phy·rin·o·gen ox·i·dase

an enzyme that catalyzes a step in porphyrin biosynthesis, reacting coproporphyrinogen III and O2 to form protoporphyrinogen IX and 2CO2. A deficiency of this enzyme will result in hereditary coproporphyria.
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The mitochondrial localization of coproporphyrinogen III oxidase.