amelogenesis imperfecta (redirected from Congenital enamel hypoplasia)

amelogenesis /am·e·lo·gen·e·sis/ (-jen´ĕ-sis) the formation of dental enamel.

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amelogenesis imperfec´ta  a hereditary condition resulting in defective development of dental enamel, marked by a brown color of the teeth; due to improper differentiation of the ameloblasts.

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amelogenesis im·per·fec·ta (mpr-fkt)

n.

A hereditary condition in which the dental enamel does not develop properly, often because of insufficient calcification. Also called enamel dysplasia.

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amelogenesis imperfecta,

a condition characterized by brown or white chalky discoloration of the teeth and resulting from either severe enamel hypocalcification or enamel hypoplasia. The condition, which is inherited as an autosomal-dominant trait, is classified according to severity: in agenesis, there is a complete lack of enamel; in enamel hypoplasia, defective matrix formation causes the enamel to be normal in hardness but deficient in quantity; and in enamel hypocalcification, defective maturation of ameloblasts results in enamel that is normal in quantity but soft and undercalcified. Also called hereditary brown enamel, hereditary enamel hypoplasia. Compare dentinogenesis imperfecta.

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amelogenesis imperfecta (am´lōjen´sis),

n a broad category of developmental disturbances in the structural formation of enamel. The disease is divided into four main types (type 1, Hypoplastic; type 2, Hypomaturation; type 3, Hypocalcified; type 4, mixed) and 15 subtypes, which range from mild to severe.

Amelogenesis imperfecta.

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amelogenesis

formation of dental enamel.

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amelogenesis imperfecta

imperfect formation of enamel, resulting in brownish coloration and friability of the teeth.