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Congenital cystic adenomatoid malformation

   Also found in: Wikipedia 0.01 sec.
Congenital cystic adenomatoid malformation (CCAM)
A condition in which one or more lobes of the fetal lungs develop into fluid-filled sacs called cysts.
Mentioned in: Prenatal Surgery


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Other causes of respiratory distress in a neonate (1,4) Diagnosis Diaphragmatic hernia Usually diagnosed prenatally Pulmonary agenesis / hypoplasia Congenital cystic adenomatoid malformation (CCAM) / sequestrated segment Congenital lobar emphysema Cardiac failure / left to right shunt / Delayed diagnosis congenital heart disease Persistent foetal circulation / patent ductus arteriosus (PDA) Pulmonary oedema
5) Differential diagnostic considerations vary based on the time of imaging and include pneumothorax, pneumatocele, atelectasis, or hypoplasia of the lung with hyperinflation of the contralateral lung, diaphragmatic hernia, and congenital cystic adenomatoid malformation.
Congenital cystic adenomatoid malformation of the lung (CCAM) is an uncommon condition characterized by cysts of various sizes lined by bronchiolar- or alveolar-like epithelium.
 
 
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