primary ciliary dyskinesia

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dyskinesia

 [dis-ki-ne´zhah]
impairment of the power of voluntary movement.
primary ciliary dyskinesia any of a group of hereditary syndromes characterized by delayed or absent mucociliary clearance from the airways; often there is also lack of motion of sperm. One variety is Kartagener's syndrome.
tardive dyskinesia an iatrogenic disorder produced by long-term administration of antipsychotic agents; it is characterized by oral-lingual-buccal dyskinesias that usually resemble continual chewing motions with intermittent darting movements of the tongue; there may also be choreoathetoid movements of the extremities. The disorder is more common in women than in men and in the elderly than in the young, and incidence is related to drug dosage and duration of treatment. In some patients symptoms disappear within several months after antipsychotic drugs are withdrawn; in others symptoms may persist indefinitely.

primary ciliary dyskinesia

an apparently autosomal recessive disorder in which mucus clearance is sluggish and bronchiectasis is prevalent and intractable. Evidence suggests the defect lies in dynein, a protein in the cilia.
Synonym(s): dyskinesia syndrome

pri·ma·ry cil·i·ar·y dys·ki·ne·si·a

(prīmar-ē silē-ar-ē diski-nēzē-ă)
Disorder inwhich mucus clearance is sluggish and bronchiectasis is prevalent and intractable.

ciliary

pertaining to or resembling cilia; used particulary in reference to certain eye structures, such as the ciliary body or muscles.

ciliary adenomas
arise from the non-pigmented inner layer of the ciliary epithelium; cause hyphema or glaucoma.
ciliary body
the thickened part of the vascular tunic of the eye, connecting choroid and iris, made up of the ciliary muscle and the ciliary processes. The processes radiate from the ciliary muscle and give attachments to ligaments supporting the lens of the eye.
ciliary body inflammation
ciliary epithelium
rostral continuation of the pars ciliaris retinae; non-pigmented, non-neural cells.
ciliary flush
dilation of deep conjunctival vessels and episcleral vessels causing perilimbal redness.
ciliary glands
sweat glands which have become arrested in their development, situated at the edge of the eyelids. Called also Moll's glands.
ciliary inflammation
cyclitis.
ciliary injection
peripheral hyperemia of the anterior ciliary vessels which produces a deep red or rose color of the corneal stroma, and must be distinguished from hyperemia of the conjunctival vessels. May spread to the perilimbic corneal tissue. Called also ciliary flush.
ciliary muscle
the smooth (mammals) or striated (birds) muscle that forms the main part of the ciliary body and and functions in accommodation of the eye.
primary ciliary dyskinesia
abnormality of ciliary function leading to diseases of respiratory and reproductive tracts including sinusitis and bronchiectasis. May be associated with cardiac displacement. See also kartagener's syndrome.
ciliary process
folded structures on the posterior aspect of the ciliary body.
Enlarge picture
Anatomy of the ciliary processes. By permission from Guyton R, Hall JE, Textbook of Medical Physiology, Saunders, 2000
ciliary reflex
movements of the pupil in accommodation.
ciliary zonules
continuations of the ciliary processes of the ciliary body connecting it to the lens. They are in close contact with the hyaloid membrane of the vitreous body.