Caroli disease

(redirected from Caroli's syndrome)

Ca·ro·li dis·ease

(kah-rō'lē), [MIM*263200]
congenital cystic dilation of the intrahepatic bile ducts, sometimes associated with intrahepatic stones and biliary obstruction; may be a part of the phenotype of infantile polycystic kidney disease.

Ca·ro·li dis·ease

, Caroli syndrome (kah-rō-lē' di-zēz', sin'drōm)
Congenital cystic dilation of the intrahepatic bile ducts, sometimes associated with intrahepatic stones and biliary obstruction.

Caroli,

Jacques, French gastroenterologist, 1902-1979.
Caroli disease - congenital cystic dilation of the intrahepatic bile ducts.
References in periodicals archive ?
5] Caroli's disease is characterized by segmental dilatation of the intrahepatic bile ducts without hepatic fibrosis as compared to Caroli's syndrome, which is defined as ectasia of the intrahepatic bile ducts with hepatic fibrosis.
Caroli's syndrome and adult polycystic kidney disease.
Caroli's Syndrome (intrahepatic ductual ectasia) is another rare congenital (from birth) disease.