Caroli disease

(redirected from Caroli's syndrome)

Ca·ro·li dis·ease

(kah-rō'lē), [MIM*263200]
congenital cystic dilation of the intrahepatic bile ducts, sometimes associated with intrahepatic stones and biliary obstruction; may be a part of the phenotype of infantile polycystic kidney disease.

Ca·ro·li dis·ease

, Caroli syndrome (kah-rō-lē' di-zēz', sin'drōm)
Congenital cystic dilation of the intrahepatic bile ducts, sometimes associated with intrahepatic stones and biliary obstruction.

Caroli,

Jacques, French gastroenterologist, 1902-1979.
Caroli disease - congenital cystic dilation of the intrahepatic bile ducts.
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References in periodicals archive ?
19 We had two patients diagnosed as Caroli's syndrome on the basis of CT scan and both were excluded from the study as we included only biopsy-proven patients of CHF.
Caroli's syndrome which has autosomal recessive or dominant inheritance occurs more frequently than in Caroli's disease.
5] Caroli's disease is characterized by segmental dilatation of the intrahepatic bile ducts without hepatic fibrosis as compared to Caroli's syndrome, which is defined as ectasia of the intrahepatic bile ducts with hepatic fibrosis.
Caroli's Syndrome (intrahepatic ductual ectasia) is another rare congenital (from birth) disease.