Caroli's disease

Caroli's disease

Hepatology A condition characterized by a diffuse distribution of intrahepatic biliary cysts and other cystic lesions–eg, medullary sponge kidneys Clinical Childhood onset–eg, jaundice, episodic fever, pain Complications Hepatic fibrosis, cirrhosis, portal HTN, esophageal bleeding, death in childhood
References in periodicals archive ?
Son Marley, six, is her inspiration, as he continues to bravely fight liver and kidney diseases portal hypertension, congenital hepatic fibrosis, Caroli's disease and polycystic kidney disease.
The differential diagnosis includes simple cysts, echinococcal cysts, liver abscesses, cystic degeneration of a liver neoplasm, Caroli's disease, posttraumatic cysts, and polycystic diseases.
2] Caroli's disease is a much less frequent condition in which there is ectasia of the intrahepatic bile ducts.
A 66-year-old male initially presented in 2002 with ascending cholangitis and was found to have intrahepatic biliary duct dilatation consistent with Caroli's disease.
Algino, who is nine years old, was diagnosed with Caroli's disease in 2005 and needs to undergo a liver transplant operation in Germany.
Also covered were some of the more important congenital biliary disorders such as Caroli's disease, as well as primary and other forms of sclerosing cholangitis.
Marley was diagnosed with portal hypertension, congenital hepatic fibrosis, Caroli's disease and polycystic kidney disease in 2013.
In ARPD, there is always involvement of the liver by fibrosis with or without ectasia of the bile ducts similar to that seen in Caroli's disease.
Type V is also known as Caroli's disease and consists of cystic dilatation of the intrahepatic biliary system.
Caroli's disease associated with pancreatic heterotopia and papillary papillomatosis.
Type V choledochal cyst according to the Todani classificiation refers to Caroli's disease.
Autosomal dominant polycystic liver disease is part of the spectrum of fibropolycystic liver diseases that are caused by congenital bile duct malformation, including bile duct hamartoma, Caroli's disease, congenital hepatic fibrosis, and choledochal cyst.