stiff heart syndrome

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stiff heart syn·drome

any condition, usually acute, that causes the heart to be restricted in diastole mainly affecting the ventricles and at one time a complication of cardiac surgery.

stiff heart syn·drome

any condition, usually acute, that causes the heart to be restricted in diastole mainly affecting the ventricles and at one time a complication of cardiac surgery.
A nonspecific term for ventricular pump failure due to restrictive heart disease
Aetiology Idiopathic, or related to amyloidosis, constrictive pericarditis due to radiation, mycosis, trauma, tuberculosis, haemochromatosis, myocardiopathy

stiff heart syndrome

Cardiology A nonspecific term for ventricular pump failure due to restrictive heart disease Clinical Chest pain, exertional dyspnea, ↑ venous pressure, extra-diastolic murmurs, hepatomegaly, ascites, edema Etiology Idiopathic, or related to amyloidosis, constrictive pericarditis due to radiation, mycosis, trauma, TB, hemochromatosis, myocardiopathy. Cf 'Stone' heart.
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References in periodicals archive ?
In lieu of flowers, donations may be made in memory of John Lazar to fund Cardiac Amyloidosis Research on behalf of Dr.
Deposition of mutant TTR in the heart may lead to cardiac amyloidosis.
Alnylam reported that the Phase II trial is aimed at evaluating the tolerability and preliminary clinical activity of ALN-TTRsc in TTR cardiac amyloidosis patients with familial amyloidotic cardiomyopathy (FAC) - which is caused by autosomal dominant mutations in the TTR gene, or senile systemic amyloidosis (SSA) - which is caused by idiopathic accumulation of wild-type TTR in the heart.
Also, within the "senile" amyloidosis category, involvement may be systemic or isolated to the heart, and two distinct subtypes of senile cardiac amyloidosis have been described.
Tissue Doppler imaging in the evaluation of patients with cardiac amyloidosis.
It has also been used to evaluate the right ventricular function in various pulmonary disease such as pulmonary hypertension (PHT), chronic pulmonary disease (CPD) and cardiac amyloidosis (9, 11, 12).
Cardiovascular involvement in rheumatoid arthritis (RA) is a rare extra-articular finding; however, pericarditis, cardiomyopathy/myocarditis, cardiac amyloidosis, coronary vasculitis, arrhythmia, valvular disorders, congestive heart failure, and ischemic heart disease may be seen in RA.
Comparison of magnetic resonance imaging versus Doppler echocardiography for the evaluation of left ventricular diastolic function in patients with cardiac amyloidosis.
Cardiac amyloidosis, a monoclonal gammopathy and a potentially misleading mutation.
In a series of 50 consecutive patients with light-chain amyloidosis and 15 patients with hereditary amyloidosis, cTnT values in patients with cardiac amyloidosis were increased compared to those in patients with light chain amyloidosis but no cardiac involvement [0.
2) Endomyocardial biopsy, though invasiye, is indicated in patients with suspected cardiac amyloidosis and unexplained diastolic heart failure, especially when extracardiac tissue is negative for amyloid.
Lewis had a rare condition called cardiac amyloidosis, a disease in which the heart is infiltrated by an abnormal protein produced elsewhere in the body.