Brugada syndrome

(redirected from Brugada)

Brugada syndrome

A family of autosomal dominant conditions which manifest themselves in young individuals—especially from southeast Asia—with no known heart problems or defects, who suffer sudden cardiac death or aborted sudden cardiac death.
 
EKG
Right bundle branch block; persistent ST-segment elevation in V1 to V3, unexplained by electrolyte disturbances; ischaemia; structural heart disease.
 
Management
Implantable defibrillator.

Brugada syndromes
Type—MIM Number—Defective gene    
Brugada-1—601144—SCN5A      
Brugada-2—611778—GPD1L-611778
Brugada-3—114205—CACNA1C-
Brugada-4—600003—CACNB2
Brugada-5—604433—KCNE3
Brugada-6—600235—SCN1B

Brugada syndrome

Cardiology A condition in which people with no known heart problems or defects suffer sudden cardiac death or aborted sudden cardiac death EKG Right bundle branch block, persistent ST-segment elevation in V1 to V3 unexplained by electrolyte disturbances, ischemia, structural heart disease Treatment Implantable defibrillator. See Long Q-T syndrome.

Brugada syndrome

(broo-gŏd′ă)
A rare hereditary syndrome, occasionally autosomal dominant, marked by right bundle branch block, S-T segment elevation in the right precordial leads of the ECG, and a high risk of sudden death from ventricular arrhythmias.
References in periodicals archive ?
Giselle Maynard, 50 and son Zachary, 13, from Radyr, were diagnosed last year with Brugada syndrome, a leading cause of sudden cardiac death.
Although the authors discussed the etiology of these ST-segment elevations, they did not mention the characteristic ST-segment elevation in the right precordial lead, which is similar to type 1 Brugada ECG patterns.
As a model of a primary rhythm disorder, Brugada syndrome (BrS may be considered as ~sensitized model~ for SCD and be relevant to the broad problem of SCD in the setting of common cardiac pathologies.
Jessica Hill, from Skelmersdale, organised the show to raise money for CRY (Cardiac Risk in the young) after her boyfriend Matt passed away two years ago from heart condition Brugada.
Brugada Syndrome), or with severe cardiac disease such as myocardial ischemia or heart failure, or structural heart disease.
She became a patron of the charity after friend Adam Donnelly died, aged 17, from a condition known as Brugada Syndrome.
Brugada syndrome is a new entity found in the last one decade and it has a familial tendency also.
We read with interest the recent review of Brugada syndrome and its anaesthetic management (1).
Later in the week, he will chair a session and speak on Early Repolarization and Brugada syndromes as causes of sudden death at the annual meeting of the International Society of Computerized Electrocardiology (ISCE) to be held at Dolce Hayes Mansion in San Jose, California.
Clara Brugada, Morena's secretary for the welfare of the people, was also present at the news conference with Batres.
Bolton wanted to make sure that Muamba would not endanger his health and sent him to Belgium to see world-renowned cardiologist Dr Pedro Brugada - who told him that it was impossible for him to play again as his heart wall was not contracting properly.