hexosaminidase (redirected from Beta-hexosaminidase B)

hexosaminidase /hex·os·amin·i·dase/ (hek?sos-ah-min´i-das)

1. any of the enzymes that cleave hexosamines or acetylated hexosamines from gangliosides or other glycosides.

2. a specific hexosaminidase acting on keratan sulfate and ganglioside GM2 and related compounds.

---

hex·os·a·min·i·dase (hks-s-mn-ds, -dz)

n.

Any of at least four enzymes, each of which is the catalyst for the removal of hexose residues from specific oligosaccharides; deficiencies of these enzymes can cause certain metabolic disorders.

---

hexosaminidase

an enzyme that catalyzes the cleavage of hexose from ganglioside GM₂. Occurs in two forms, A and B. Deficiency occurs in GM₂gangliosidosis of dogs, cats and pigs.