Arnold-Chiari deformity


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Related to Arnold-Chiari deformity: Chiari malformation

deformity

 [de-for´mĭ-te]
distortion of any part or of the body in general; called also malformation.
Arnold-Chiari deformity a congenital anomaly in which the cerebellum and medulla oblongata protrude down into the cervical spinal canal through the foramen magnum; it is almost always associated with meningomyelocele and hydrocephalus.
Madelung's deformity radial deviation of the hand secondary to overgrowth of the distal ulna or shortening of the radius.

Ar·nold-Chi·a·ri mal·for·ma·tion

(ar'nŏld kē-ah'rē), [MIM*207950]
malformed posterior fossa structures associated with caudad traction and displacement of the rhombencephalon as caused by tethering of the spinal cord; may be accompanied in some cases by spina bifida and associated anomalies such as meningomyelocele; usually multifactorial in inheritance.

Arnold-Chiari malformation

A congenital compression deformity of the lower brain, which is characterised by herniation of the cerebellar tonsils and distal medulla oblongata through the foramen magnum into the spinal canal. The Arnold-Chiari malformation is accompanied by compression of the 4th ventricle and firm adhesions at the cisterna magna.

Arnold,

Julius, German pathologist, 1835-1915.
Arnold bodies - small portions or minute fragments of erythrocytes.
Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformation
Arnold-Chiari malformation - malformed posterior fossa structures. Synonym(s): Arnold-Chiari deformity; Arnold-Chiari syndrome; cerebellomedullary malformation syndrome
Arnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation

Chiari,

Hans, German pathologist, 1851-1916.
Arnold-Chiari deformity - Synonym(s): Arnold-Chiari malformation
Arnold-Chiari malformation - see under Arnold, Julius
Arnold-Chiari syndrome - Synonym(s): Arnold-Chiari malformation
Budd-Chiari syndrome - Synonym(s): Chiari syndrome
Chiari disease - Synonym(s): Chiari syndrome
Chiari net - abnormal fibrous or lacelike strands in the right atrium.
Chiari syndrome - thrombosis of the hepatic vein with great enlargement of the liver and extensive development of collateral vessels, intractable ascites, and severe portal hypertension. Synonym(s): Budd-Chiari syndrome; Budd syndrome; Chiari-Budd syndrome; Chiari disease; Rokitansky disease (2)
Chiari-Budd syndrome - Synonym(s): Chiari syndrome
Chiari II syndrome - elongation of medulla and cerebellar tonsils and vermis with displacement through the foramen magnum into the upper spinal canal.

Arnold-Chiari deformity

central nervous system deformity often associated with spina bifida