arrhythmogenic right ventricular dysplasia type 9

(redirected from ARVD9)

arrhythmogenic right ventricular dysplasia type 9

An autosomal dominant condition (OMIM:609040) characterised by fibro-fatty degeneration of the right ventricular myocardium, electromechanical instability and sudden death.

Molecular pathology
Defects in PKP2 cause arrhythmogenic right ventricular dysplasia type 9.