ALCAPA


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ALCAPA

Anomalous origin of the left coronary artery from the pulmonary artery. A rarely identified congenital cardiac defect which presents in adulthood as malignant ventricular arrhythmias and sudden cardiac death.
Management Re-routing of the coronary arteries; cryotherapy to treat the ventricular tachycardia.
References in periodicals archive ?
When enlarged right coronary artery, left ventricular enlargement and contraction failure are observed on echocardiogram, ALCAPA should be suspected.
Conclusively, ALCAPA can be treated surgically and can present asymptomatically at advanced ages, if well developed collateral arteries are present as in our patient.
The steal phenomenon caused by ALCAPA causes significant left ventricular myocardial compromise and is associated with a high morbidity in infants.
Since the left coronary artery appeared to originate from the pulmonary artery (figure 2), ALCAPA syndrome was considered in the patient and cardiac catheterization and angiography were decided to be performed.
Although ALCAPA syndrome is observed rarely, if it is not treated, is has a high mortality rate during the first 1-2 years of life.
Diagnosis of ALCAPA which is a treatable condition in children with dilated cardiomyopathy is very important.
Although the first signs generally occur after the first 2-3 months of life, clinical, telecardiographical and ECG findings should be examined, clues on ECHO related to ALCAPA should be investigated carefully and early treatment should be provided in newborn patients presenting with DCM.
The youngster has the rare condition ALCAPA and had to have a lifesaving op