ALCAPA


Also found in: Acronyms.

ALCAPA

Anomalous origin of the left coronary artery from the pulmonary artery. A rarely identified congenital cardiac defect which presents in adulthood as malignant ventricular arrhythmias and sudden cardiac death.
Management Re-routing of the coronary arteries; cryotherapy to treat the ventricular tachycardia.
References in periodicals archive ?
This study aimed to retrospectively illustrate the perioperative clinical features, therapy experience, and midterm outcomes after surgical correction, and to determine the value of left ventricular ejection fraction (LVEF) and myocardial viability in differentiating critically ill patients among infants and children with ALCAPA.
She underwent surgery for atrial septal defect at 10 years of age and the repair of suspected right coronary artery (RCA) fistula into the right ventricle according to cardiac catheterization, while the ALCAPA was not detected.
The advanced development in cardiac CT and magnetic resonance imaging (MRI) provides noninvasive diagnostic tools for ALCAPA.
Because it is so rare, no long-term studies of adults with corrected ALCAPA are available, but the prognosis is generally good in children, and Drs.
14) reported that they false negatively observed the origin of the left coronary artery to be normal in their series of three patients and the origin of the left coronary artery should be demonstrated echocardiographically or angiographic evaluation should be done in patients in whom ALCAPA is suspected (14).
The steal phenomenon caused by ALCAPA causes significant left ventricular myocardial compromise and is associated with a high morbidity in infants.
However, systematic assessments of the LV function and size, MR, and complications of patients with ALCAPA managed with left coronary artery (LCA) re-implantation are limited.
1 ALCAPA is usually an isolated cardiac anomaly but in rare cases it may be associated with other congenital heart diseases.
A diagnosis of ALCAPA syndrome was made as a result of diagnostic angiography and with clinical electrocardiographical and echocardiographical findings in a 28 days old patient with dilated cardiomyopahty (DCM) and congestive cardiac failure.
Ella Mae came into the world with a condition that baffled doctors known as ALCAPA - or anomalous left coronary artery from the pulmonary artery.